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Surgical treatment of isolated unilateral absence of pulmonary artery with pulmonary hypertension

Part of: Surgery

Published online by Cambridge University Press:  08 March 2021

Moyu Hasegawa*
Affiliation:
Department of Cardiovascular Surgery, Osaka Women’s and Children’s Hospital, Osaka, Japan
Shigemitsu Iwai
Affiliation:
Department of Cardiovascular Surgery, Osaka Women’s and Children’s Hospital, Osaka, Japan
Kazuhiko Ishimaru
Affiliation:
Department of Cardiovascular Surgery, Osaka Women’s and Children’s Hospital, Osaka, Japan
*
Author for correspondence: Moyu Hasegawa, MD, Department of Cardiovascular Surgery, Osaka Women’s and Children’s Hospital, 840 Murodocho, Izumi, Osaka594-1101, Japan. Tel: +81 725 561220; Fax: +81 725 565682. E-mail: moyu6698@gmail.com

Abstract

A one-and-a-half-month-old patient with isolated unilateral absence of the right proximal pulmonary artery with prominent left pulmonary hypertension was diagnosed using CT. Medication therapy was initiated first. Left pulmonary artery pressure decreased after the initiation of medication therapy, and single-stage reconstruction of the right pulmonary artery was performed. The patient is asymptomatic 14 months postoperatively.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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