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Sick sinus syndrome: a family study

Published online by Cambridge University Press:  11 September 2013

Natalia Rogińska*
Affiliation:
Klinika Kardiologii Instytutu, “Pomnik – Centrum Zdrowia Dziecka” (Cardiology Clinic, The Children's Memorial Health Institute), Head of Department: Wanda Kawalec, Poland
Katarzyna Bieganowska
Affiliation:
Klinika Kardiologii Instytutu, “Pomnik – Centrum Zdrowia Dziecka” (Cardiology Clinic, The Children's Memorial Health Institute), Head of Department: Wanda Kawalec, Poland
*
Correspondence to: Lek. med. N. Rogińska, Klinika Kardiologii Instytutu, “Pomnik –Centrum Zdrowia Dziecka”, al. Dzieci Polskich 20, 04-730 Warszawa, Poland. Tel: +22 815 73 77; mobile: 604086542; E-mail: natalia@roginska.pl

Abstract

A case of related individuals affected by sick sinus syndrome is presented in this study. The clinical and electrocardiographic signs of sinus node dysfunction and the most common causes of this disease are presented. Subsequently, the article includes descriptions of sinus node disease in three related children as well as details of the disease in their relatives. A literature review of the genetics of familial sinus node dysfunction concludes the study.

Type
Images in Congenital Cardiac Disease
Copyright
Copyright © Cambridge University Press 2013 

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