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Septum primum malposition defect and inferior sinus venosus defect: a rare association

Published online by Cambridge University Press:  02 October 2014

Deepa Prasad ,
Christopher Snyder  and
Ravi Ashwath
Deepa Prasad
Affiliation:
Case Western Reserve University, Rainbow Babies and Children’s Hospital, Cleveland, Ohio, United States of America
Christopher Snyder
Affiliation:
Case Western Reserve University, Rainbow Babies and Children’s Hospital, Cleveland, Ohio, United States of America
Ravi Ashwath*
Affiliation:
Case Western Reserve University, Rainbow Babies and Children’s Hospital, Cleveland, Ohio, United States of America
*
Correspondence to: R. Ashwath, MD, Division of Pediatric Cardiology, Rainbow Babies and Children’s Hospital, 11100 Euclid Avenue, MS RBC 6011, Cleveland, OH 44106, United States of America. Tel: +216 844 3528; Fax: +216 201 4650; E-mail: Ravi.Ashwath@UHhospitals.org
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Abstract

We present a case of a 2-year-old girl who presented with respiratory distress and umbilical abscess, and was found to have an inferior sinus venosus defect, malposition of the atrial septum primum, absent septum secundum, and anomalous drainage of the right upper and lower pulmonary veins to the right atrium.

Keywords

Inferior sinus venosus defectseptum primum malposition defectpartial anomalous pulmonary venous drainage
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 7 , October 2015 , pp. 1389 - 1392
Copyright
© Cambridge University Press 2014 

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