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Rhabdomyoma of the interventricular septum presenting as a Brugada phenocopy

Published online by Cambridge University Press:  04 May 2011

Timothy Nguyen ,
John Smythe  and
Adrian Baranchuk
Timothy Nguyen
Affiliation:
Division of Cardiology, Kingston General Hospital, Queen's University, Canada
John Smythe
Affiliation:
Division of Cardiology, Kingston General Hospital, Queen's University, Canada
Adrian Baranchuk*
Affiliation:
Division of Cardiology, Kingston General Hospital, Queen's University, Canada
*
Correspondence to: Dr A. Baranchuk, MD FACC, Associate Professor of Medicine, Cardiac Electrophysiology and Pacing, Kingston General Hospital K7L 2V7, Queen's University, Canada. Tel: 613 549 6666 ext 3801; Fax: 613 548 1387; E-mail: barancha@kgh.kari.net
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Abstract

Brugada syndrome is a channelopathy characterised electrocardiographically by distinctive coved ST-segment elevation in the right precordial leads and is associated with a predisposition for sudden death secondary to ventricular arrhythmias in otherwise healthy patients. Previously known as Brugada-like patterns, Brugada phenocopies include agents and conditions that mimic true Brugada syndrome, presenting with an acquired Brugada Type-1 ECG pattern. We describe the first reported case of a 17-month-old female with an asymptomatic rhabdomyoma of the interventricular septum that presented as a Brugada phenocopy.

Keywords

Brugada syndromeBrugada ECG-like patternintracardiac tumour
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 5 , 09 September 2011 , pp. 591 - 594
Copyright
Copyright © Cambridge University Press 2011

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