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Recognising ligamentous atresia in double aortic arch

Published online by Cambridge University Press:  13 December 2022

Tyler Bendrick ,
Dillon Polito ,
Randy Richardson ,
Robert H. Anderson Open the ORCID record for Robert H. Anderson [Opens in a new window]  and
Deepa Prasad Open the ORCID record for Deepa Prasad [Opens in a new window]
Tyler Bendrick
Affiliation:
Creighton University School of Medicine, Phoenix Regional Campus, Phoenix, AZ, USA
Dillon Polito
Affiliation:
Creighton University School of Medicine, Phoenix Regional Campus, Phoenix, AZ, USA
Randy Richardson
Affiliation:
Department of Radiology, Creighton University School of Medicine, Phoenix, AZ, USA
Robert H. Anderson
Affiliation:
Newcastle University Biosciences Institute, Institute of Medical Genetics, Newcastle upon Tyne, UK
Deepa Prasad*
Affiliation:
Creighton University School of Medicine, Phoenix Regional Campus, Phoenix, AZ, USA Department of Pediatric Cardiology, Banner Children’s at Desert Medical Center, Mesa, AZ, USA
*
Author for correspondence: Dr. Deepa Prasad, University of Arizona College of Medicine, Phoenix, Department of Pediatric Cardiology, Banner Children’s at Desert Medical Center, Mesa, AZ, USA. E-mail: Pras.deepa@gmail.com
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Abstract

Ligamentous atresia of the left side of a double arch distal to the left subclavian artery is a rare form of vascular ring, which can easily be confused, on transthoracic echocardiography, with the right-sided aortic arch when there is mirror-imaged branching. Because of its rapid acquisition, computed tomographic angiography with three-dimensional reconstruction has now become the modality of choice for accurate diagnosis of the various forms of double aortic arch. It can be performed without sedation in any age group, including neonates. It provides excellent visualisation of the aortic arch and its branching pattern, thus permitting accurate diagnosis and surgical planning. We present a case series of six children with this rare vascular ring assessed using CT, highlighting their outcomes.

Keywords

Double aortic archCT angiographyvascular ring
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 7 , July 2023 , pp. 1209 - 1212
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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