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Rare associations of tetralogy of Fallot with anomalous left coronary artery from pulmonary artery and totally anomalous pulmonary venous connection

Published online by Cambridge University Press:  08 April 2016

Supratim Sen ,
Suresh G. Rao  and
Snehal Kulkarni
Supratim Sen*
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
Suresh G. Rao
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
Snehal Kulkarni
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
*
Correspondence to: S. Sen, Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Four Bunglows, Andheri West, Mumbai 400053, India. Tel: +91 8080329189; Fax: +91 33 23598189; E-mail: supratim80@gmail.com
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Abstract

We describe the cases of two patients with tetralogy of Fallot, aged 4 years and 8 months, who were incidentally detected to have concomitant anomalous left coronary artery from pulmonary artery and total anomalous pulmonary venous connection, respectively, on preoperative imaging. They underwent surgical correction with good mid-term outcomes. In this study, we discuss the embryological basis, physiological effects, and review the literature of these two unusual associations. Awareness of these rare associations will avoid missed diagnoses and consequent surgical surprises.

Keywords

Tetralogy of Fallottotal anomalous pulmonary venous connectionanomalous left coronary artery from pulmonary arteryunusual associations of tetralogy of Fallot
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Issue 5 , June 2016 , pp. 1017 - 1020
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Copyright
© Cambridge University Press 2016 

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References

1. Siwik, E, Erenberg, F, Zahka, KG, Goldmuntz, E. Tetralogy of Fallot. In: Allen HD, Driscoll DJ, Shaddy RE, Feltes TF (eds). Moss and Adams’ Heart Disease in Infants, Children, and Adolescents, 7th edn. Lippincott Williams & Wilkins, Philadelphia, PA, 2008: 888–905.Google Scholar
2. Perloff, JK, Marelli, AJ. Clinical Recognition of Congenital Heart Disease, 6th edn. Elsevier Saunders, Philadelphia, PA, 2012.Google Scholar
3. Bitar, FF, Kveselis, DA, Smith, FC, Byrum, CJ, Quaegebeur, JM. Double-outlet right ventricle (tetralogy of Fallot type) associated with anomalous origin of the left coronary artery from the right pulmonary artery: report of successful total repair in a 2-month-old infant. Pediatr Cardiol 1998; 19: 361–362.CrossRefGoogle Scholar
4. Kurup, RP, Daniel, R, Kumar, RK. Anomalous origin of the left coronary artery from the pulmonary artery in infancy with preserved left ventricular function: potential pitfalls and clues to diagnosis. Ann Pediatr Cardiol 2008; 1: 65–67.Google Scholar
5. Talwar, S, Choudhary, SK, Shivaprasad, MK, et al. Tetralogy of Fallot with total anomalous pulmonary venous drainage. Ann Thoracic Surg 2008; 86: 1937–1940.Google Scholar
6. Quintessenza, JA, Jacobs, JP, Morell, VO, Giroud, JM, Boucek, RJ. Initial experience with a bicuspid polytetrafluoroethylene pulmonary valve in 41 children and adults: a new option for right ventricular outflow tract reconstruction. Ann Thorac Surg 2005; 79: 924–931.Google Scholar
7. Anderson, RH, Brown, NA, Moorman, AFM. Development and structures of the venous pole of the heart. Dev Dyn 2006; 235: 2–9.Google Scholar
8. Bajolle, F, Zaffran, S, Losay, J, Ou, P, Buckingham, M, Bonnet, D. Conotruncal defects associated with anomalous pulmonary venous connections. Arch Cardiovasc Dis 2009; 102: 105–110.Google Scholar
9. Buckingham, M, Meilhac, S, Zaffran, S. Building the mammalian heart from two sources of myocardial cells. Nat Rev Genet 2005; 6: 826–835.Google Scholar