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Meandering right pulmonary vein associated with severe and progressive “idiopathic-like” pulmonary hypertensive vascular disease

Published online by Cambridge University Press:  16 September 2015

Sofia Cuenca Open the ORCID record for Sofia Cuenca [Opens in a new window] ,
Montserrat Bret  and
Maria Jesus del Cerro
Sofia Cuenca*
Affiliation:
Cardiology Department, Hospital Universitario Puerta de Hierro Majadahonda, Madrid, Spain
Montserrat Bret
Affiliation:
Pediatric Radiology Department, Hospital Universitario La Paz, Madrid, Spain
Maria Jesus del Cerro
Affiliation:
Pediatric Cardiology Department, Hospital Universitario Ramon y Cajal, Madrid, Spain
*
Correspondence to: S. Cuenca, Cardiology Department, Hospital Universitario Puerta de Hierro Majadahonda, Manuel de Falla 1, Majadahonda, Madrid 28222, Spain. Tel: +34 913369027; Fax: +34 913368685; E-mail: somalea25@yahoo.es
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Abstract

Congenital anomalies of the pulmonary veins are rare. Meandering right pulmonary vein, considered a part of the Scimitar syndrome spectrum, is often an incidental finding during chest imaging. We present the case of a 4-year-old girl diagnosed with meandering pulmonary vein, who developed pulmonary hypertensive disease with an aggressive course, in spite of absence of hypoxia or elevated pulmonary wedge pressure.

Keywords

Meandering pulmonary veinscimitar syndromepulmonary hypertension
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Supplement 3 , March 2016 , pp. 615 - 618
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Copyright
© Cambridge University Press 2015 

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References

1. Woodring, JH, Howard, TA, Knaga, JF. Congenital pulmonary venolobar syndrome revisited. Radiographics 1994; 14: 349–369.Google Scholar
2. Hamad, AM. Congenital pulmonary venolobar syndrome: value of multidetector computed tomography in preoperative assessment. Ann Thorac Med 2012; 7: 165–167.CrossRefGoogle ScholarPubMed
3. Rodrigues, MA, Ritchie, G, Murchison, JT. Incidental meandering right pulmonary vein, literature review and proposed nomenclature revision. World J Radiol 2013; 5: 215–219.CrossRefGoogle ScholarPubMed
4. Sanger, PW, Taylor, FH, Robicesek, F. The “scimitar syndrome”: diagnosis and treatment. Arch Surg 1963; 86: 580–587.Google Scholar
5. Goodman, LR, Jamshidi, A, Hipona, FA. Meandering right pulmonary vein simulating the Scimitar syndrome. Chest 1972; 62: 510–512.Google Scholar
6. Cerro, MJ, Abman, S, Diaz, G, et al. A consensus approach to the classification of pediatric pulmonary hypertensive vascular disease: report from the PVRI Pediatric Taskforce, Panama 2011. Pulm Circ 2011; 1: 286–298.Google Scholar
7. Ivy, DD, Abman, SH, Barst, RJ, et al. Pediatric pulmonary hypertension. J Am Coll Cardiol 2013; 62 (Suppl 25): D117–D126.CrossRefGoogle ScholarPubMed
8. Salerno, T, Guccione, P, Malena, S, Cutrera, R. Horseshoe lung associated with unique left pulmonary vein: an unreported association. Pediatr Cardiol 2010; 31: 905–907.Google Scholar
9. Dusenbery, SM, Geva, T, Seale, A, et al. Outcome predictors and implications for management of scimitar syndrome. Am Heart J 2013; 165: 770–777.CrossRefGoogle ScholarPubMed
10. Endo, M, Yamaki, S, Hata, M, Saiki, Y, Tabayashi, K. Pulmonary vascular changes induced by unilateral pulmonary venous obstruction. Pediatr Cardiol 2002; 23: 420–425.Google Scholar
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