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Hypoplastic left heart with intact atrial septum and levoatriocardinal vein: a challenge in identifying aortic arch branches

Published online by Cambridge University Press:  17 January 2014

Govinda Paudel*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Hospitals and Clinics, University of Iowa, Iowa, United States of America
Benton Y. Ng
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Hospitals and Clinics, University of Iowa, Iowa, United States of America
Ian H. Law
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Hospitals and Clinics, University of Iowa, Iowa, United States of America
*
Correspondence: Dr G. Paudel, Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Hospitals and Clinics, 200 Hawkins Drive, Iowa City, Iowa 52242, United States of America. Tel: +00 1 319 356 4995; Fax: +00 1 319 356 4693; E-mail: govinda-paudel@uiowa.edu

Abstract

The levoatriocardinal vein provides alternative egress from the left atrium to the systemic veins in left-sided obstructive lesions. Although rare, it has been described in association with hypoplastic left heart syndrome. We report a case of hypoplastic left heart syndrome with levoatriocardinal vein and aberrant right subclavian artery where cardiac magnetic resonance imaging/angiography proved to be a valuable imaging modality for pre-operative evaluation.

Type
Brief Reports
Copyright
© Cambridge University Press 2014 

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