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Effective control of refractory pulmonary hypertension with iloprost inhalation in an infant with congenital absence of the right pulmonary artery: a case report

Published online by Cambridge University Press:  15 January 2024

Chu-Yuan Hsiao Open the ORCID record for Chu-Yuan Hsiao [Opens in a new window]  and
Wen-Hsien Lu Open the ORCID record for Wen-Hsien Lu [Opens in a new window]
Chu-Yuan Hsiao
Affiliation:
Department of Pediatrics, Kaohsiung Veterans General Hospital, Kaohsiung, Taiwan
Wen-Hsien Lu*
Affiliation:
Department of Pediatrics, Kaohsiung Veterans General Hospital, Kaohsiung, Taiwan Fooyin University, Kaohsiung, Taiwan Institute of Biomedical Sciences, National Sun Yat-sen University, Kaohsiung, Taiwan
*
Corresponding author: Wen-Hsien Lu; Email: lu6802@gmail.com
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Abstract

Unilateral absence of the pulmonary artery is a rare congenital cardiovascular anomaly that can lead to pulmonary hypertension and poor outcomes. We report the case of a 1-month-old infant with isolated unilateral absence of the pulmonary artery and severe pulmonary hypertension on the right and left sides, respectively. The patient was unresponsive to multiple medications for pulmonary hypertension, and surgical revascularisation was unfeasible. However, iloprost inhalation was effective.

Keywords

Congenital absence of pulmonary arterycyanosisiloprostnitrate oxidepulmonary hypertension
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 3 , March 2024 , pp. 690 - 693
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Copyright
© The Author(s), 2024. Published by Cambridge University Press

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