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Diagnosis and management of congenital right pulmonary venous atresia

Published online by Cambridge University Press:  23 October 2009

I. Ricardo Argueta-Morales ,
Ruchira Garg  and
William M. DeCampli
I. Ricardo Argueta-Morales
Affiliation:
Congenital Heart Institute at Arnold Palmer Hospital and Miami Children’s Hospital, Arnold Palmer Hospital for Children, Orlando, Florida
Ruchira Garg
Affiliation:
Congenital Heart Institute at Arnold Palmer Hospital and Miami Children’s Hospital, Miami Children’s Hospital, Miami, Florida
William M. DeCampli*
Affiliation:
Congenital Heart Institute at Arnold Palmer Hospital and Miami Children’s Hospital, Arnold Palmer Hospital for Children, Orlando, Florida
*
Correspondence to: William M. DeCampli, MD, PhD, Congenital Heart Institute, Arnold Palmer Hospital for Children, 50 West Sturtevant Street, Orlando, Florida, USA 32806. Phone: 407-649-6907; Fax: 321-841-4260; E-mail: william.decampli@orlandohealth.com
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Abstract

Congenital unilateral pulmonary venous atresia is a rare anatomical defect. Patients present with pulmonary symptoms, and diagnosis may be ellusive. Pulmonary arterial wedge angiography is the gold standard with which to achieve diagnosis, and surgical intervention is often required for symptomatic patients.

Keywords

Heart defectsunilateral pulmonary venous atresiacongenital malformations
Type
Brief Reports
Information
Cardiology in the Young , Volume 19 , Issue 6 , December 2009 , pp. 648 - 651
Copyright
Copyright © Cambridge University Press 2009

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References

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