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An unusual case of pulmonary atresia with ventricular septal defect and multiple major aortopulmonary collateral arteries: undiagnosed until adulthood

Published online by Cambridge University Press:  09 January 2023

Feyza Sönmez Topcu ,
Baran Simsek Open the ORCID record for Baran Simsek [Opens in a new window]  and
Arda Ozyuksel Open the ORCID record for Arda Ozyuksel [Opens in a new window]
Feyza Sönmez Topcu
Affiliation:
Department of Radiology, Aydin University, Medical Park Florya Hospital, Istanbul, Turkey
Baran Simsek*
Affiliation:
Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey
Arda Ozyuksel
Affiliation:
Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey Department of Cardiovascular Surgery, Biruni University, Istanbul, Turkey
*
Author for correspondence: Baran Simsek, Department of Cardiovascular Surgery, Medicana International Hospital, Istanbul, Turkey. E-mail: simsekbaran7@gmail.com
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Abstract

Pulmonary atresia and ventricular septal defect with major aortopulmonary collateral arteries is an extremely complex, heterogeneous, and rare anomaly. This group of patients may not be able to survive until adulthood without any interventions or treatment. Although surgical management of patients diagnosed in newborn, infant, or early childhood is clear, treatment of patients diagnosed in adulthood still remains a significant problem. The pre-operative clinical status, imaging methods, and operative findings might be helpful for planning the most appropriate management. Herein, we report a unique case of pulmonary atresia and ventricular septal defect with major aortopulmonary collateral arteries who remained asymptomatic until the age of 18 years.

Keywords

Pulmonary atresiaventricular septal defectCHDsurgical anastomosispolytetrafluoroethylene
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 8 , August 2023 , pp. 1445 - 1447
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Copyright
© The Author(s), 2023. Published by Cambridge University Press

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