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An unusual case of a solitary cardiac myofibroma causing severe right ventricular outflow tract obstruction in an infant

Published online by Cambridge University Press:  26 October 2020

Prashant K. Minocha*
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, New York Grossman University School of Medicine, New York, USA Hassenfeld Children’s Hospital at NYU Langone, New York, USA
Fei Chen
Affiliation:
Department of Pathology, New York University Grossman School of Medicine, New York, USA
Joseph J. Maleszewski
Affiliation:
Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, MN, USA
Achiau Ludomirsky
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, New York Grossman University School of Medicine, New York, USA Hassenfeld Children’s Hospital at NYU Langone, New York, USA
Ralph Mosca
Affiliation:
Hassenfeld Children’s Hospital at NYU Langone, New York, USA Division of Pediatric Cardiothoracic Surgery, New York University Grossman School of Medicine, New York, USA
T. K. Susheel Kumar
Affiliation:
Hassenfeld Children’s Hospital at NYU Langone, New York, USA Division of Pediatric Cardiothoracic Surgery, New York University Grossman School of Medicine, New York, USA
*
Author for correspondence: Prashant K. Minocha, 401 East 34th Street, 4th Floor, Pediatric Cardiology, New York 10016, USA. Tel: +1 212 263 3079; Fax: +1 212 263 8301. E-mail: prashant.minocha@nyulangone.org

Abstract

Cardiac tumours are relatively uncommon, particularly in children. Myofibroma is an extremely rare variety of cardiac tumour, which nearly always arises in the context of infantile myofibromatosis. Herein, we present a case of a solitary cardiac myofibroma causing right ventricular outflow tract obstruction in a 2-month-old male infant.

Type
Brief Report
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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