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Trans-catheter closure of an unusual type of Abernethy malformation in a child presenting with severe pulmonary hypertension

Published online by Cambridge University Press:  12 December 2023

Santosh Wadile Open the ORCID record for Santosh Wadile [Opens in a new window] ,
Ashishkumar Banpurkar Open the ORCID record for Ashishkumar Banpurkar [Opens in a new window]  and
Snehal Kulkarni
Santosh Wadile*
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Centre for Child Heart Care and Training in Pediatric Cardiac Skills, Navi Mumbai, Maharashtra, India
Ashishkumar Banpurkar
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Centre for Child Heart Care and Training in Pediatric Cardiac Skills, Navi Mumbai, Maharashtra, India
Snehal Kulkarni
Affiliation:
Department of Pediatric Cardiology, Sri Sathya Sai Sanjeevani Centre for Child Heart Care and Training in Pediatric Cardiac Skills, Navi Mumbai, Maharashtra, India
*
Corresponding author: Santosh Wadile; Email: santosh_wadile@yahoo.co.in
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Abstract

Abernethy malformation is a congenital extra-hepatic porto-systemic shunt. This malformation is characterized by an abnormal connection between the portal vein or its branches and one of the systemic veins. Though rare, this anomaly can lead to pulmonary hypertension. Drainage of Abernethy malformation into coronary sinus is extremely rare. We describe a child with Abernethy malformation with unusual drainage into coronary sinus. The abnormal channel was successfully closed by trans-catheter technique with normalisation of pulmonary arterial pressures.

Keywords

Abernethy malformationporto-systemic shuntpulmonary hypertensiondevice closureporto-pulmonary syndrome
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 2 , February 2024 , pp. 436 - 438
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Copyright
© The Author(s), 2023. Published by Cambridge University Press

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References

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