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Surgical approach to a rare case of double-outlet right ventricle and aortopulmonary window

Published online by Cambridge University Press:  04 March 2015

Robert D. Tunks ,
R. Dennis Steed  and
Andrew J. Lodge
Robert D. Tunks
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, Duke University Medical Center, Durham, North Carolina, United States of America
R. Dennis Steed
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, East Carolina University, Greenville, North Carolina, United States of America
Andrew J. Lodge*
Affiliation:
Department of Surgery, Division of Cardiovascular and Thoracic Surgery, Duke University Medical Center, Durham, North Carolina, United States of America
*
Correspondence to: Dr A. J. Lodge, Department of Surgery, Duke University Medical Center, Box 3340, Durham, NC 27710, United States of America. Tel: +1 919 681 2343; Fax: +1 919 681 4907; E-mail: andrew.lodge@duke.edu
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Abstract

Although the spectrum of physiology seen in infants and children with double-outlet right ventricle is broad, this anatomy in combination with an aortopulmonary window is extremely rare. We present an interesting case of an infant prenatally diagnosed with this rare CHD. To our knowledge, this is the first report of complete repair in the neonatal period for such a combination of defects.

Keywords

Aortopulmonary windowcardiothoracic surgeryCHDdouble-outlet right ventricle
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Supplement 1 , January 2016 , pp. 172 - 174
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Copyright
© Cambridge University Press 2015 

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References

1. Pettersen, MD, Du, W, Skeens, ME, Humes, RA. Regression equations for calculation of z scores of cardiac structures in a large cohort of healthy infants, children, and adolescents: an echocardiographic study. J Am Soc Echocardiogr 2008; 21: 922–934.CrossRefGoogle Scholar
2. Hartge, DR, Niemeyer, L, Axt-Fliedner, R, et al. Prenatal detection and postnatal management of double outlet right ventricle (DORV) in 21 singleton pregnancies. J Matern Fetal Neonatal Med 2012; 25: 58–63.Google Scholar
3. Kadohira, I, Miyakoshi, K, Yoshimura, Y. Prenatal images of the aortopulmonary window with an interrupted aortic arch. Pediatr Cardiol 2013; 34: 1288–1289.CrossRefGoogle ScholarPubMed
4. Anderson, RH, McCarthy, K, Cook, AC. Continuing medical education. Double outlet right ventricle. Cardiol Young 2001; 11: 329–344.Google Scholar
5. Kutsche, LM, Van Mierop, LH. Anatomy and pathogenesis of aorticopulmonary septal defect. Am J Cardiol 1987; 59: 443–447.Google Scholar
6. Kirby, ML, Waldo, KL. Neural crest and cardiovascular patterning. Circ Res 1995; 77: 211–215.Google Scholar
7. Cabano, R, Lombardi, G, Mannarino, S, Cerbo, RM, Manzoni, P, Stronati, M. A newborn with double-outlet right ventricle and aortopulmonary window associated with maternal phenylketonuria: a first case report. Acta Paediatr 2011; 100: 318.CrossRefGoogle ScholarPubMed
8. Cavalini, JF, Aiello, VD, Guedes de Souza, P, et al. Double outlet right ventricle with intact atrial septum and restrictive ventricular septal defect: an analysis of two cases. Pediatr Cardiol 1998; 19: 490–494.Google Scholar

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