Hostname: page-component-7479d7b7d-jwnkl Total loading time: 0 Render date: 2024-07-11T09:19:38.281Z Has data issue: false hasContentIssue false
  • English
  • Français

Myotonic dystrophy presenting as atrial flutter in childhood

Published online by Cambridge University Press:  20 January 2005

Kenji Suda ,
Masahiko Matsumura  and
Yuji Hayashi
Kenji Suda
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Tenri Hospital, Tenri City, Japan
Masahiko Matsumura
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Tenri Hospital, Tenri City, Japan
Yuji Hayashi
Affiliation:
Department of Internal medicine, Kinan Hospital, Mihama town, Mie, Japan
Get access Rights & Permissions [Opens in a new window]

Abstract

A 12-year-old boy presented with tachycardia and cardiomegaly. An electrocardiogram showed atrial flutter with a ventricular rate of 170 beats/min. The echocardiogram showed left ventricular dilation, with decreased contractility. Electromyography confirmed the diagnosis of myotonic dystrophy. The atrial flutter was converted to sinus rhythm by electroversion, leading to restoration of normal cardiac function. Our case illustrates that atrial flutter can be an early sign of the cardiac complications of myotonic dystrophy in childhood.

Keywords

Paediatricsatrial arrhythmiascardiomyopathy
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 1 , February 2004 , pp. 89 - 92
Copyright
© 2004 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Hageman AT, Gabreels FJ, Liem KD, Renkawek K, Boon JM. Congenital myotonic dystrophy: a report on thirteen cases and a review of the literature. J Neurol Sci 1993; 115: 95–101.Google Scholar
Phillips MF, Harper PS. Cardiac disease in myotonic dystrophy. Cardiovasc Res 1997; 33: 13–22.Google Scholar
McLay JS, Norris A, Kerr F. Could it be myotonic dystrophy? Myotonic dystrophy presenting with atrial flutter. Scott Med J 1992; 37: 149–150.Google Scholar
Rechavia E, Strasberg B, Agmon J. Unusual cardiac manifestations in a patient with myotonic muscular dystrophy. Int J Cardiol 1986; 11: 349–352.Google Scholar
Pickering JG, Guiraudon C, Klein GJ. Focal right atrial dysplasia and atrial flutter in a patient with myotonic dystrophy. Pacing Clin Electrophysiol 1989; 12: 1317–1323.Google Scholar
Morgenlander JC, Nohria V, Saba Z. EKG abnormalities in pediatric patients with myotonic dystrophy Pediatr Neurol 1993; 9: 124–126.Google Scholar
Fish FA, Benson DW Jr. Disorders of cardiac rhythm and conduction. In: Allen HD, Gutgesell HP, Clark EB, Driscoll DJ (eds). Moss and Adams' Heart disease in infants, children, and adolescents. 6th edn. Lippincott Williams & Wilkins, Philadelphia, PA, 2001: pp 482–533.