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Reversible Wall Enhancement in Pediatric Cerebral Arteriopathy

Published online by Cambridge University Press:  02 December 2014

Eric T. Payne
Affiliation:
Division of Neurology, Departments of Pediatrics and Clinical Neurosciences, University of Calgary and the Alberta Children's Hospital, Calgary, Alberta, Canada
Xing-Chang Wei
Affiliation:
Department of Radiology, University of Calgary and the Alberta Children's Hospital, Calgary, Alberta, Canada
Adam Kirton*
Affiliation:
Division of Neurology, Departments of Pediatrics and Clinical Neurosciences, University of Calgary and the Alberta Children's Hospital, Calgary, Alberta, Canada
*
Calgary Pediatric Stroke Program, Pediatrics and Clinical Neuroscience, Faculty of Medicine, University of Calgary, Alberta Children's Hospital, 2888 Shaganappi Trail NW, Calgary, Alberta, T3B 6A8, Canada
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A previously well and developmentally normal five-year-old right-handed girl, presented with acute left-sided weakness and dysarthria. Investigations confirmed an acute right lenticulostriate stroke secondary to probable childhood primary angiitis of the CNS(cPACNS), including evidence of vessel wall enhancement (Figure). Despite extensive investigations, no alternative etiology for her stroke was detected. After three weeks of steroids, the child improved and the vessel wall enhancement resolved. Moderate hemiparesis, hemidystonia, and behavioural sequelae are present at 18-month follow-up.

Type
Neuroimaging Highlights
Copyright
Copyright © Canadian Neurological Sciences Federation 2011

References

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