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Neuropsychological profile of a male psychiatric patient with a Morgagni-Stewart-Morel syndrome

Published online by Cambridge University Press:  10 November 2014

Aksel Hansen ,
Liliana Engelhardt ,
Wolfgang Pleschutznig ,
Gerhard Dammann  and
Stephanie Vietze
Aksel Hansen*
Affiliation:
Department of Psychiatry, Psychiatrische Dienste Thurgau, Switzerland
Liliana Engelhardt
Affiliation:
Department of Psychiatry, Psychiatrische Dienste Thurgau, Switzerland
Wolfgang Pleschutznig
Affiliation:
Department of Psychiatry, Psychiatrische Dienste Thurgau, Switzerland
Gerhard Dammann
Affiliation:
Department of Psychiatry, Psychiatrische Dienste Thurgau, Switzerland
Stephanie Vietze
Affiliation:
Department of Psychiatry, Psychiatrische Dienste Thurgau, Switzerland
*
Aksel Hansen, Psychiatrische Dienste Thurgau, Seeblickstrasse 3, Postfach 154 8596, Münsterlingen, Switzerland. Tel: 0041716864032;Fax: 0041716864035; E-mail: hansenak@web.de
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Abstract

In 1765 Giovanni Morgagni described a syndrome consisting of hyperostosis frontalis interna (HFI), obesity and hirsutism. In 1928 Stewart and in 1930 Morel added neuropsychiatric symptoms, e.g. depression and dementia, which led to the definition of the Morgagni-Stewart-Morel Syndrome (MSM). Although mostly women were characterized in literature no gender specifity is demanded. This case report presents the rare case of a 66 year old male psychiatric patient with Morgagni-Stewart-Morel Syndrome. The patient complained of loss of concentration and difficulties with activities of daily living. Admission diagnosis was an opioid misuse on the basis of a chronic pain syndrome. In this case report we are describing clinical features, the patient history and technical (MRI) and neuropsychological tests. Although severe psychiatric symptoms and neuropsychological deficits are commonly seen in these patients, our patient showed only mild symptoms. This case reports shows the possibility of a male patient with MSM. If MSM is a separate entity or just an epiphenomena of hormone dysregulation should be investigated in further studies.

Keywords

hyperostosis frontalis internahormone dysregulationMorgagni-Stewart-Morel syndromeneuropsychological testing
Type
Case Report
Information
Acta Neuropsychiatrica , Volume 27 , Issue 1 , February 2015 , pp. 60 - 64
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Copyright
© Scandinavian College of Neuropsychopharmacology 2014 

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