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Chapter 21 - Epilepsy Syndromes

from Part III - Specific Conditions

Published online by Cambridge University Press:  24 June 2021

Neville M. Jadeja
Affiliation:
University of Massachusetts Medical School
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Summary

Epilepsy syndromes (electroclinical syndromes) are well-recognized groupings of clinical (seizure types) and EEG features that occur together. Each syndrome typically shares a common age of onset, deficits (intellectual dysfunction), treatment, and prognosis. Syndromes are classified based on their onset, epilepsy type (focal, generalized, or mixed), and development of epileptic encephalopathy (disorder in which epileptic activity contributes to severe impairments in cognition and behavior). Relatively benign syndromes are typically associated with focal, generalized tonic clonic (GTC), typical absences, and myoclonic seizures. Epileptic encephalopathies are typically associated with atonic, tonic, atypical absences, and epileptic spasms in addition to the preceding seizure types.

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Information
How to Read an EEG , pp. 195 - 213
Publisher: Cambridge University Press
Print publication year: 2021

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References

Scheffer, IE, Berkovic, S, Capovilla, G, et al. ILAE classification of the epilepsies: position paper of the ILAE Commission for Classification and Terminology. Epilepsia. 2017 Apr;58(4):512–21.CrossRefGoogle ScholarPubMed
Miles, DK, Holmes, GL. Benign neonatal seizures. Journal of Clinical Neurophysiology. 1990 Jul;7(3):369–79.CrossRefGoogle ScholarPubMed
Donat, JF. Topical review article: the age-dependent epileptic encephalopathies. Journal of Child Neurology. 1992 Jan;7(1):721.CrossRefGoogle Scholar
Vigevano, F. Benign familial infantile seizures. Brain and Development. 2005 Apr 1;27(3):172–7.CrossRefGoogle ScholarPubMed
Caraballo, RH, Fontana, E, Darra, F, et al. Migrating focal seizures in infancy: analysis of the electroclinical patterns in 17 patients. Journal of Child Neurology. 2008 May;23(5):497506.Google Scholar
Dravet, C, Bureau, M. Benign myoclonic epilepsy in infancy. Epileptic Syndromes in Infancy, Childhood and Adolescence. 2005;4:7788.Google Scholar
Quigg, M. EEG pearls. Mosby Elsevier, New York; 2006.Google Scholar
Donald Shields, W, Carter Snead, O III. Benign epilepsy with centrotemporal spikes. Epilepsia. 2009 Sep;50:1015.CrossRefGoogle Scholar
Yalçin, AD, Kaymaz, A, Forta, H. Childhood occipital epilepsy: seizure manifestations and electroencephalographic features. Brain and Development. 1997 Sep 1;19(6):408–13.Google ScholarPubMed
Mattson, RH. Overview: idiopathic generalized epilepsies. Epilepsia. 2003 Mar;44:26.CrossRefGoogle ScholarPubMed
Tassinari, CA, Rubboli, G, Gardella, EL, Michelucci, RO. Epilepsy with myoclonic absences. Epilepsy in Children. 2004 Feb;27:189–94.Google Scholar
Stephani, U. The natural history of myoclonic astatic epilepsy (Doose syndrome) and Lennox‐Gastaut syndrome. Epilepsia. 2006 Nov;47:53–5.Google Scholar
Camfield, P, Camfield, C. Febrile seizures and genetic epilepsy with febrile seizures plus (GEFS+). Epileptic Disorders. 2015 Jun;17(2):124–33.CrossRefGoogle ScholarPubMed
Bertrand, D, Picard, F, Le Hellard, S, et al. How mutations in the nAChRs can cause ADNFLE epilepsy. Epilepsia. 2002 Jun;43:112–22.CrossRefGoogle ScholarPubMed
Michelucci, R, Pasini, E, Nobile, C. Lateral temporal lobe epilepsies: clinical and genetic features. Epilepsia. 2009 May;50:52–4.CrossRefGoogle ScholarPubMed
Gambardella, A, Labate, A, Giallonardo, A, Aguglia, U. Familial mesial temporal lobe epilepsies: clinical and genetic features. Epilepsia. 2009 May;50:55–7.Google Scholar
Dibbens, LM, De Vries, B, Donatello, S, et al. Mutations in DEPDC5 cause familial focal epilepsy with variable foci. Nature Genetics. 2013 May;45(5):546.CrossRefGoogle ScholarPubMed
Vining, EP, Freeman, JM, Brandt, J, Carson, BS, Uematsu, S. Progressive unilateral encephalopathy of childhood (Rasmussen’s syndrome): a reappraisal. Epilepsia. 1993 Jul;34(4):639–50.Google Scholar
Arroyo, S, Lesser, RP, Gordon, B, et al. Mirth, laughter and gelastic seizures. Brain. 1993 Aug 1;116(4):757–80.Google Scholar
Gastaut, H, Poirier, F, Payan, H, Salamon, G, Toga, M, Vigouroux, MH. HHE syndrome hemiconvulsions, hemiplegia, epilepsy. Epilepsia. 1959 Jan;1(1–5):418–47.CrossRefGoogle Scholar

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