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Successful bone-anchored hearing aid implantation in a patient with osteogenesis imperfecta

  • M B Coutinho (a1), C Marques (a2), G J Mendes (a3) and C Gonçalves (a4)

Abstract

Objective:

To report a case of successful bone-anchored hearing aid implantation in an adult patient with type III osteogenesis imperfecta, which is commonly regarded as a contraindication to this procedure.

Case report:

A 45-year-old man with type III osteogenesis imperfecta presented with mixed hearing loss. There was a mild sensorineural component in both ears, with an air–bone gap between 45 and 50 dB HL. He was implanted with a bone-anchored hearing aid. The audiological outcome was good, with no complications and good implant stability (as measured by resonance frequency analysis).

Conclusion:

To our knowledge, this is the first recorded case of bone-anchored hearing aid implantation in a patient with osteogenesis imperfecta.

Copyright

Corresponding author

Address for correspondence: Dr Miguel Bebiano Coutinho, Otolaryngology Department, Hospital Lusíadas Porto, Unidade de Otorrinolaringologia, Avenida da Boavista, 171, 4050-115 Porto, Portugal E-mail: coutinho.mb@gmail.com

References

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Keywords

Successful bone-anchored hearing aid implantation in a patient with osteogenesis imperfecta

  • M B Coutinho (a1), C Marques (a2), G J Mendes (a3) and C Gonçalves (a4)

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