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Lipoamide Dehydrogenase in Friedreich's Ataxia Fibroblasts

  • S. B. Melançon (a1), M. Potier (a1), L. Dallaire (a1), G. Fontaine (a1), B. Grenier (a1), B. Lemieux (a1), G. Geoffroy (a1) and A. Barbeau (a1)...

Summary:

Lipoamide dehydrogenase was measued in cultivated skin fibroblasts from twelve patients with Friedreich's ataxia and nine normal controls. No difference in specific activity, subcellular distribution and Vmax or Km was observed between patients and controls.

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Copyright

Corresponding author

Clinical Research Institute of Montreal, 110 Pine Avenue West, Montreal, Quebec, Canada H2W 1R7

References

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Lipoamide Dehydrogenase in Friedreich's Ataxia Fibroblasts

  • S. B. Melançon (a1), M. Potier (a1), L. Dallaire (a1), G. Fontaine (a1), B. Grenier (a1), B. Lemieux (a1), G. Geoffroy (a1) and A. Barbeau (a1)...

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