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Susac's syndrome: a rare cause of fluctuating sensorineural hearing loss

Published online by Cambridge University Press:  29 June 2007

Neil D. Bateman ,
Ian J. M. Johnson  and
Kevin P. Gibbin
Neil D. Bateman*
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, University Hospital, Nottingham, UK
Ian J. M. Johnson
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, University Hospital, Nottingham, UK
Kevin P. Gibbin
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, University Hospital, Nottingham, UK
*
Address for correspondence: Mr Neil Bateman, Department of Otolaryngology – Head and Neck Surgery, University Hospital, Queen's Medical Centre, Nottingham NG7 2UH
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Abstract

Susac's syndrome is extremely rare and is characterized by the clinical triad of encephalopathy, retinal artery occlusion and deafness. A case of this rare syndrome is presented and for the first time the fluctuating nature of the hearing loss is demonstrated. The site and nature of the hearing loss has been investigated. The value of neural hearing loss as a method of monitoring the clinical severity is discussed.

Keywords

Hearing loss, sensorineural
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 111 , Issue 11 , November 1997 , pp. 1072 - 1074
Copyright
Copyright © JLO (1984) Limited 1997

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