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Cochlear implantation of a patient with multiple sclerosis: case report and systematic review

Published online by Cambridge University Press:  15 October 2021

J Routila ,
J O Karhu  and
J Salonen
J Routila*
Affiliation:
Department of Audiology, Turku University Hospital, Turku, Finland Department of Otorhinolaryngology – Head and Neck Surgery, University of Turku, Turku, Finland
J O Karhu
Affiliation:
Department of Radiology, Turku University Hospital, Turku, Finland
J Salonen
Affiliation:
Department of Audiology, Turku University Hospital, Turku, Finland Department of Otorhinolaryngology – Head and Neck Surgery, University of Turku, Turku, Finland
*
Author for correspondence: Mr Johannes Routila, Department of Audiology, Turku University Hospital, Kiinamyllynkatu 4-8, TurkuFI-20521, Finland E-mail: johannes.routila@utu.fi
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Abstract

Background

Cochlear implantation can be used when a patient's hearing cannot satisfactorily be improved after optimised hearing aid fitting. However, in patients with a cochlear nerve or brain disorder affecting hearing, the benefits of cochlear implants are not so straightforward.

Methods

This paper describes a 58-year-old patient suffering from multiple sclerosis and profound sensorineural hearing loss, rehabilitated with a cochlear implant. Literature concerning cochlear implantation in demyelinating conditions was systematically reviewed using PubMed/Medline and Web of Science databases.

Results

The patient's cochlear implantation was successful, with speech discrimination scores remaining above 90 per cent for eight years post-operatively. No previous cases of cochlear implantation with multiple sclerosis related hearing loss have been reported, despite the high incidence of hearing loss in multiple sclerosis patients.

Conclusion

This paper demonstrates that multiple sclerosis lesions should not be an exclusion criterion in an otherwise suitable candidate for cochlear implantation.

Keywords

Multiple SclerosisAcoustic TumorHearing LossCochlear ImplantsRehabilitation
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 136 , Issue 2 , February 2022 , pp. 176 - 180
Copyright
Copyright © The Author(s), 2022. Published by Cambridge University Press on behalf of J.L.O. (1984) LIMITED.

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Footnotes

Mr J Routila takes responsibility for the integrity of the content of the paper

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