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Transcatheter closure of Abernethy malformation associated with interrupted inferior caval vein and other systemic venous anomalies

Published online by Cambridge University Press:  29 July 2021

Samir Shakya Open the ORCID record for Samir Shakya [Opens in a new window] ,
Anita Saxena  and
Sivasubramanian Ramakrishnan
Samir Shakya
Affiliation:
Pediatric Cardiology, Department of Cardiology, All India Institute of Medical Sciences, New Delhi110029, India
Anita Saxena*
Affiliation:
Department of Cardiology, All India Institute of Medical Sciences, New Delhi110029, India
Sivasubramanian Ramakrishnan
Affiliation:
Department of Cardiology, All India Institute of Medical Sciences, New Delhi110029, India
*
Author for correspondence: Dr A. Saxena, MD, DM, Department of Cardiology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110029, India. Tel: +91 01126594861. E-mail: anitasaxena@hotmail.com
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Abstract

Abernethy malformation is a rare entity. We report a 5-year-old boy presenting with severe pulmonary hypertension in whom Abernethy malformation and inferior caval vein interruption were diagnosed by CT angiography. In addition, the iliac veins were thrombosed with multiple venous collateral drainage. This abnormal venous anatomy caused difficulty in device closure of the Abernethy malformation, which was successfully closed using a vascular plug.

Keywords

Abernethy malformationinferior caval vein interruptiondevice closure
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 2 , February 2022 , pp. 337 - 339
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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