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Tetralogy of Fallot with congenital diaphragmatic hernia and left lung hypoplasia: assessment of the adequacy of the peripheral pulmonary vascular growth after hernia repair

Published online by Cambridge University Press:  15 September 2011

Hong Ju Shin ,
Won Kyoung Jhang  and
Tae Jin Yun
Hong Ju Shin
Affiliation:
Cardiovascular Surgery, Konkuk University Medical Center, University of Ulsan, Seoul, South Korea
Won Kyoung Jhang
Affiliation:
Pediatric Cardiology, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, South Korea
Tae Jin Yun*
Affiliation:
Division of Pediatric Cardiac Surgery, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, South Korea
*
Correspondence to: Dr T.-J. Yun, MD, PhD, Divisional Head, Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan, 388-1 Pungnap-dong Songpa-gu, Seoul 138-736, South Korea. Tel: +82 2 3010 3589; Fax: +82 2 3010 6811; E-mail: tjyun@amc.seoul.kr
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Abstract

Congenital diaphragmatic hernia is a life-threatening condition frequently associated with various congenital cardiac diseases. In congenital diaphragmatic hernia associated with tetralogy of Fallot, central pulmonary artery size of the affected side may not reflect the capacitance of peripheral pulmonary vascular beds. We report a case of congenital diaphragmatic hernia associated with tetralogy of Fallot, which was repaired after assessing the adequacy of the pulmonary vascular beds by intra-operative pulmonary blood flow study.

Keywords

Congenital cardiac diseasecardiac surgerycongenital diaphragmatic hernia
Type
Brief Reports
Information
Cardiology in the Young , Volume 22 , Issue 2 , 02 March 2012 , pp. 235 - 238
Copyright
Copyright © Cambridge University Press 2011

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