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Repair of a mixed form of supracardiac total anomalous pulmonary venous connection

Published online by Cambridge University Press:  03 November 2020

Yuki Kawasaki Open the ORCID record for Yuki Kawasaki [Opens in a new window] ,
John N. Dentel ,
Henry L. Walters III ,
James M. Galas  and
Daisuke Kobayashi
Yuki Kawasaki
Affiliation:
Division of Cardiology, Children’s Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA Division of Paediatric Cardiology, Osaka City General Hospital Paediatric Medical Center, Osaka, Japan
John N. Dentel
Affiliation:
Division of Cardiovascular Surgery, Children’s Hospital of Michigan, Department of Surgery, Wayne State University School of Medicine, Detroit, MI, USA
Henry L. Walters III
Affiliation:
Division of Cardiovascular Surgery, Children’s Hospital of Michigan, Department of Surgery, Wayne State University School of Medicine, Detroit, MI, USA
James M. Galas
Affiliation:
Division of Cardiology, Children’s Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA
Daisuke Kobayashi*
Affiliation:
Division of Cardiology, Children’s Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA
*
Author for correspondence: D. Kobayashi, MD, Division of Cardiology, Children’s Hospital of Michigan, 3901 Beaubien Blvd, Detroit, MI 48201-2119, USA. Tel: +1 313 745 5481; Fax: +1 313 993 0894. E-mail: dkobayas@dmc.org
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Abstract

Total anomalous pulmonary venous connection is a rare congenital heart defect. We report an infant with a mixed form of supracardiac TAPVC, in whom all pulmonary veins, except the right upper, entered a pulmonary venous confluence that is connected to a vertical vein and drained into the superior vena caval–right atrial junction. Several segmental right upper pulmonary veins entered the superior vena cava, superior to the entry of the vertical vein. Surgical repair consisted of the Warden procedure combined with direct anastomosis of the vertical vein to the left atrium. Separate pulmonary venous drainage pathways decreased the risk of post-operative pulmonary venous obstruction. Our patient had an uneventful post-operative course and encouraging 2-month follow-up echocardiography. Careful follow-up is warranted to detect post-operative complications, including obstruction of the pulmonary venous and cavoatrial anastomoses.

Keywords

Supracardiac total anomalous pulmonary venous connectionWarden proceduredirect anastomosisneonatal repair
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 2 , February 2021 , pp. 300 - 302
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Copyright
© The Author(s), 2020. Published by Cambridge University Press

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References

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