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Repair in infancy of right aortic arch with aberrant left brachiocephalic artery in the setting of a variant of the hypoplastic left heart syndrome

Published online by Cambridge University Press:  21 January 2005

Suvro S. Sett
Affiliation:
British Columbia Children's Hospital, Vancouver, BC, Canada
John B. Mawson
Affiliation:
British Columbia Children's Hospital, Vancouver, BC, Canada
George G. S. Sandor
Affiliation:
British Columbia Children's Hospital, Vancouver, BC, Canada

Abstract

A right aortic arch, with a retroesophageal transverse arch and an aberrant left brachiocephalic artery, is a rare anomaly by itself. When combined with severe mitral stenosis and hypoplasia of the left ventricle, it is rarer still. We describe the diagnosis and treatment of this rare anomaly in an infant using a modification of the Norwood operation.

Type
Brief Report
Copyright
© 2004 Cambridge University Press

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