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Persistence of the hepatic venous plexus with underdevelopment of the inferior caval vein: implications in the management of complex congenital heart disease

Published online by Cambridge University Press:  19 August 2008

Gordon Gladman ,
Ian Adatia  and
Robert M. Freedom
Gordon Gladman
Affiliation:
Division of Cardiology, The Hospital for Sick Children, Tronto, Canada
Ian Adatia*
Affiliation:
Division of Cardiology, The Hospital for Sick Children, Tronto, Canada
Robert M. Freedom
Affiliation:
Division of Cardiology, The Hospital for Sick Children, Tronto, Canada
*
Dr. Ian Adatia, Division of Cardiology, The Hospital for Sick Children, 555, University Avenue, Toronto, Canada, M5G 1X8. Tel: 416-813-6140, Fax. 416-813-7547
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Summary

We report two cases with persistence of the hepatic venous complex, underdevelopment of the inferior caval vein and azygos continuation to the superior caval vein. We suggest that the hepatic venous complex is a true congenital malformation rather than the result of passive enlargement of venous channels subsequent to high venous pressures. Preoperative diagnosis is important in patients with complex congenital heart disease undergoing palliative venous redirection procedures if a postoperative right-to-left shunt and cyanosis are to be avoided.

Keywords

Systemic venous anomalieshepatic venous plexusazygos continuation
Type
Brief Reports
Information
Cardiology in the Young , Volume 8 , Issue 2 , April 1998 , pp. 243 - 246
Copyright
Copyright © Cambridge University Press 1998

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