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Non-confluent pulmonary arteries in a patient with pulmonary atresia and intact ventricular septum: ? a 5th aortic arch with a systemic-to-pulmonary arterial connection

Published online by Cambridge University Press:  19 August 2008

Astolfo Serra Jr ,
Francisco Chamie  and
R.M. Freedom
Astolfo Serra Jr
Affiliation:
Department of Pediatric Cardiology, Instituto Estadual de Cardiologia Aloysio de Castro, Rio de Janeiro Brasil and CARPE-Cardiologia Pediatrica e Fetal- Rio de JaneiroBrasil
Francisco Chamie
Affiliation:
Division of Pediatric Cardiology, Department of Cardiology, Hospital dos Servidores do Estado-MS, Rio de Janeiro Brasil, and CARPE-Cardiologia Pediatrica e Fetal- Rio de JaneiroBrasil
R.M. Freedom*
Affiliation:
Division of Cardiology, Department of Pediatrics, the Hospital for Sick Children, Toronto and University of Toronto Faculty of Medicine, Toronto, Canada
*
Robert M. Freedom, MD, FRCPC, The Hospital for Sick Children, 555 University Avenue, Toronto, Ontario, CanadaM5G 1X8. Tel: 1–416–8136132; Fax: 1–416–8137547, E-mail: rfreedom@sickkids.on.ca
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Abstract

Major abnormalities of pulmonary circulation are uncommon in the patient with pulmonary atresia and intact ventricular septum. Non-confluent pulmonary arteries have only rarely been described in this setting. In this case report, we describe a patient in whom the pulmonary arteries are non-confluent, with the right pulmonary artery supplied through a right-sided arterial duct, and the left pulmonary artery most likely through a fifth aortic arch, thus providing a systemic-to-pulmonary arterial connection. We discuss the various forms of non-confluent pulmonary arteries in the setting of pulmonary atresia and intact ventricular septum.

Keywords

Pulmonaryarteryatresiaventricular septum
Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 4 , July 2000 , pp. 419 - 422
Copyright
Copyright © Cambridge University Press 2000

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