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A new approach to hypoplastic left heart syndrome with an intact atrial septum

Published online by Cambridge University Press:  18 June 2007

Claire Barker*
Affiliation:
Department of Anaesthesia, St. Thomas’ Hospital, London, United Kingdom
Franco Moscuzza
Affiliation:
Department of Anaesthesia, St. Thomas’ Hospital, London, United Kingdom
David Anderson
Affiliation:
Department of Cardiothoracic Surgery, St. Thomas’ Hospital, London, United Kingdom
*
Correspondence to: Claire Barker, Department of Anaesthesia, St. Thomas’ Hospital, London, SE1 7EH, United Kingdom. Tel: +44 (0)207 188 0652; Fax: +44 (0)207 188 0628; E-mail: cbarker@doctors.org.uk

Abstract

An intact atrial septum places infants with hypoplasia of the left heart into a group with an extremely high rate of mortality. We report a neonate, diagnosed antenatally, who was delivered by Caesarian section in the cardiac theatre, urgently placed onto cardiopulmonary bypass, and who then underwent an atrial septectomy and banding of both pulmonary arteries. After stablilisation, his arterial duct was stented, completing the first stage of hybrid palliation.

Type
Brief Report
Copyright
Copyright © Cambridge University Press 2007

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