Hostname: page-component-76fb5796d-wq484 Total loading time: 0 Render date: 2024-04-27T01:57:19.062Z Has data issue: false hasContentIssue false
  • English
  • Français

Life-long follow-up in congenitally corrected transposition

Published online by Cambridge University Press:  01 November 2007

Wei-Jen Shih ,
Jacqueline A. Noonan  and
Alberto Mazzoleni
Wei-Jen Shih*
Affiliation:
Nuclear Medicine Service, Lexington Veterans Administration Medical Center, Lexington, Kentucky, United States of America Department of Diagnostic Radiology, College of Medicine, University of Kentucky, Lexington, Kentucky, United States of America
Jacqueline A. Noonan
Affiliation:
Department of Pediatrics, College of Medicine, University of Kentucky, Lexington, Kentucky, United States of America
Alberto Mazzoleni
Affiliation:
Cardiovascular Section, Medicine Service, United States of America Division of Cardiovascular Medicine, Department of Internal Medicine, College of Medicine, University of Kentucky, Lexington, Kentucky, United States of America
*
Correspondence to: Dr Wei-Jen Shih, Nuclear Medicine Service, Lexington VA Medical Center, 1101 Veterans Drive, Lexington, KY 40502, USA. Tel: +1 859 381 5928; Fax: +1 850 381 5934; E-mail: wshih0@uky.edu
Get access Rights & Permissions [Opens in a new window]

Abstract

A male patient with congenitally corrected transposition, with no associated cardiac malformations, was diagnosed in childhood and followed until his death at age 28. He underwent two cardiac gated single photon emission computed tomographies over a two year period, which demonstrated progression of ischaemia and reduction of systolic function. The findings suggest that, when the systemic ventricle is perfused by the morphologically right coronary artery, there may be inadequate perfusion to supply any subsequent extensive hypertrophy.

Keywords

Congenital heart diseasedual isotope cardiac single photon emission computed tomographic studymyocardial perfusionleft ventricle ejection fractioncoronary angiography
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 6 , December 2007 , pp. 681 - 684
Copyright
Copyright © Cambridge University Press 2007

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Rutledge, JM, Nihill, MR, Fraser, CD, Smith, OE, Mcmathon, CJ, Bezod, LI. Outcome of 121 patients with congenitally corrected transportation of the great arteries. Pediatric Cardiol 2002; 23: 137–145.CrossRefGoogle Scholar
2. Wu, JC, Child, JS. Common congenital heart disorders in adults. Curr Probl Cardiol 2004; 29: 641–700.CrossRefGoogle ScholarPubMed
3. Graham, TP, Bernard, YD, Mellen, BG, et al. . Long-term outcome in congenitally corrected transposition of the great arteries – a multi-institutional study. J Am Coll Cardiol 2000; 36: 255–261.CrossRefGoogle ScholarPubMed
4. Nebyh, DE, Crubb, NR. Congenital heart disease: Grown up congenital heart disease – clinical problems. In: Cardiology – An illustrative color text. Elsevier/Churchill Livingstone, London, New York, Toronto, 2005, pp 144–145.Google Scholar
5. Duarte, PS, Matusmoto, A, Moises, VA, Tebexreni, A, Mastrocolla, LE. Tc-99 m MIBI SPECT in a patient with congenitally corrected transposition of the great arteries and situs solitus. Clin Nucl Med 2002; 27: 530–531.CrossRefGoogle Scholar
6. Schmidt, M, Theissen, P, Moka, D, Voth, E, Schmitter, H-T, Schicha, H. Tc-99 m MIBI SPECT correlated with magnetic resonance imaging for cardiac evaluation of a patient with congenitally corrected transposition of the great arteries (L-TGA). Clin Nucl Med 2001; 26: 714–715.CrossRefGoogle Scholar
7. Hornung, TS, Bernard, EJ, Jaeggi, ET, Howman-Giles, RB, Celermajer, DS, Hawker, RE. Myocardial perfusion and associated systemic ventricular dysfunction in congenitally corrected transposition of the great arteries. Heart 1998; 80: 322–326.CrossRefGoogle ScholarPubMed