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Echocardiography of hypoplastic left heart syndrome

Published online by Cambridge University Press:  13 December 2011

Thieu Nguyen ,
Michelle Miller ,
Javier Gonzalez ,
Katherine Nardell ,
James Galas ,
John B. John ,
Stan Timofeev ,
Rich Lambou ,
Kathryn Douglas  and
Gerald Marx
Thieu Nguyen*
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Michelle Miller
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Javier Gonzalez
Affiliation:
Pediatric Cardiology Associates/Pediatrix Medical Group, Saint Petersburg and Tampa, Florida, United States of America
Katherine Nardell
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
James Galas
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
John B. John
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America Pediatric Cardiology Associates/Pediatrix Medical Group, Saint Petersburg and Tampa, Florida, United States of America
Stan Timofeev
Affiliation:
Department of Cardiology, University of Florida, Tampa, Florida, United States of America
Rich Lambou
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Kathryn Douglas
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Gerald Marx
Affiliation:
Department of Cardiology, Children's Hospital Boston, Boston, Massachusetts, United States of America
*
Correspondence to: Dr T. P. Nguyen, MD, All Children's Hospital – Heart Institute of Florida, 2nd Floor Outpatient Care Center, 601 5th Street South, Saint Petersburg, Florida 33701, United States of America. Tel: +1 727 767 3333; Fax: +1 727 767 8990; E-mail: Thieu.nguyen@allkids.org
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Abstract

Echocardiography is critical in the assessment of patients with hypoplastic left heart syndrome. Fundamental techniques and standardised approaches are useful when evaluating patients with hypoplastic left heart syndrome prenatally, after birth, and before the Norwood operation (Stage 1); after the Norwood operation, before and after the superior cavopulmonary anastomosis (Stage 2); before and after the Fontan operation (Stage 3); and for chronic surveillance after the Fontan operation. From foetal assessment to ongoing surveillance after the Fontan procedure, echocardiography remains the primary technique for cardiac monitoring in this growing population of children and adults.

Keywords

Hypoplastic left heart syndromeechocardiographycongenital cardiac disease
Type
Original Article
Information
Cardiology in the Young , Volume 21 , Issue S2: A Holistic Approach to Hypoplastic Left Heart Syndrome and other evolving challenges in Pediatric and Congenital Cardiac Disease , 13 December 2011 , pp. 28 - 37
Copyright
Copyright © Cambridge University Press 2011

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References

1.Tchervenkov, CI, Jacobs, JP, Weinberg, PM, et al. The nomenclature, definition and classification of hypoplastic left heart syndrome. Cardiology in the Young, 2006; 16: 339–368.CrossRefGoogle ScholarPubMed
2.Michelfelder, EC, Gomez, CA, Border, W, Gottliebson, W, Franklin, C. Predictive value of fetal pulmonary venous flow patterns in identifying the need for atrial septoplasty in the newborn with hypoplastic left ventricle. Circulation 2005; 112: 2974–2979. Epub 31 October 2005.CrossRefGoogle ScholarPubMed
3.Szwast, A, Tian, Z, McCann, M, Donaghue, D, Rychik, J. Vasoreactive response to maternal hyperoxygenation in the fetus with Hypoplastic Left Heart Syndrome. Circ Cardiovasc Imaging 2010; 3: 172–178.CrossRefGoogle ScholarPubMed
4.Berg, C, Gembruch, O, Gembruch, U, Geipel, A. Doppler indices of the middle cerebral artery in fetuses with cardiac defects theoretically associated with impaired cerebral oxygen delivery in utero: is there a brain-sparing effect? Ultrasound Obstet Gynecol 2009; 34: 666–672.CrossRefGoogle Scholar
5.Rychik, J, Bush, DM, Spray, TL, et al. Assessment of pulmonary/systemic blood flow ratio after first-stage palliation for hypoplastic left heart syndrome: Development of a new index with the use of Doppler echocardiography. J Thoracic Cardiovasc Surg 2000; 120: 81–87.Google Scholar
6.Snider, AR, Serwer, GA, Ritter, SB. Echocardiography in Pediatric Heart Disease. Baltimore, MD: Mosby 1997.Google Scholar
7.Cohen, MS, Marino, BS, McElhinney, DB, et al. Neo-aortic root dilatation and valve regurgitation up to 21 years after staged reconstruction for hypoplastic left heart syndrome. Journal of the American College of Cardiology 2003; 42: 533–540.Google ScholarPubMed