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Diagnosis and natural history of isolated congenital pulmonary regurgitation in fetal life

Published online by Cambridge University Press:  19 August 2008

Kazuhiro Mori ,
Yasunobu Hayabuchi  and
Yasuhiro Kuroda
Kazuhiro Mori*
Affiliation:
Department of Pediatrics, School of Medicine, University of Tokushima, Tokushima, Japan
Yasunobu Hayabuchi
Affiliation:
Department of Pediatrics, School of Medicine, University of Tokushima, Tokushima, Japan
Yasuhiro Kuroda
Affiliation:
Department of Pediatrics, School of Medicine, University of Tokushima, Tokushima, Japan
*
Kazuhiro Mori, MD, Department of Pediatrics, School of Medicine, University of Tokushima, 3–18–15 Kuramoto-cho, Tokushima-city, Tokushima, 770–8503, Japan Tel. 81–886–33–7135, Fax: 81–886–31–8697
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Abstract

We describe a rare instance of isolated pulmonary regurgitation caused by a dysplastic pulmonary valve which was detected prenatally. Fetal echocardiography demonstrated severe pulmonary regurgitation, and progressive cardiomegaly because of right ventricular volume overload. After birth, conservative therapy was successful in alleviating the pulmonary vascular resistance, and the pulmonary regurgitation gradually decreased.

Keywords

Congenital pulmonary regurgitationdysplastic pulmonary valvefetal echocardiography
Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 2 , March 2000 , pp. 162 - 165
Copyright
Copyright © Cambridge University Press 2000

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