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Diagnosis and management of congenital umbilical arteriovenous malformation

Published online by Cambridge University Press:  02 December 2020

Shweta Bakhru Open the ORCID record for Shweta Bakhru [Opens in a new window] ,
Vijayanand Jamalpuri  and
Nageswara Rao Koneti Open the ORCID record for Nageswara Rao Koneti [Opens in a new window]
Shweta Bakhru
Affiliation:
Department of Pediatric cardiology, Rainbow Children’s Heart Institute, Hyderabad, India
Vijayanand Jamalpuri
Affiliation:
Department of Neonatology, Rainbow Children’s Hospital, Hyderabad, India
Nageswara Rao Koneti*
Affiliation:
Department of Pediatric cardiology, Rainbow Children’s Heart Institute, Hyderabad, India
*
Author for correspondence: Dr Nageswara Rao Koneti, Department of Pediatric cardiology, Rainbow Children’s Heart Institute, Road No. 10, Banjara Hills, Hyderabad 500034 India. Tel: +91 040 43681000; Fax: +91 40 4466 5555. E-mail: drkoneti@yahoo.com
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Abstract

An 8-day-old neonate was presented with severe respiratory distress and diagnosed as primary pulmonary hypertension of the newborn on functional echocardiogram. Evaluation showed bounding pulse, enlarged umbilical cord, and bruit over the periumbilical region. Transthoracic echocardiography and CT angiogram showed a large fistulous communication between the umbilical vein and artery suggestive of congenital umbilical arteriovenous malformation leading to high-output cardiac failure and pulmonary artery hypertension. The patient was stabilised with medications and ventilation. Transcatheter closure of communication was done using coils, vascular plug, and KONAR-MFTM device. The patient improved from heart failure soon after the procedure and thriving normally at 6 months of follow-up.

Keywords

Arteriovenous malformationumbilical anomalieshigh-output failureendovascular therapy
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 3 , March 2021 , pp. 493 - 495
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Copyright
© The Author(s), 2020. Published by Cambridge University Press

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