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Aortic vasculopathy with aneurysm: a rare cause of fetal hydrops

Published online by Cambridge University Press:  19 August 2008

Teo Nissen
Affiliation:
Department of Pathology, University of California, San Francisco, CA, USA
Norman H. Silverman
Affiliation:
Department of Pediatrics, University of California. San Francisco, CA, USA
Philip C. Ursell*
Affiliation:
Department of Pathology, University of California, San Francisco, CA, USA
*
Philip C Ursell, MD, Department of Pathology, University of California, San Francisco, CA 94143–0506 Tel (415) 476–6912, Fax (415) 476–9672, E-mail pursell@itsa.ucsf.edu

Abstract

An hydropic fetus seen at 28-weeks gestation had a saccular aortic aneurysm in the descending thoracic aorta. Histology disclosed marked fibrointimal hyperplasia, thrombus, and attenuation of the tunica media. The remainder of the descending thoracic aorta showed fibrointimal hyperplasia. We speculate that the narrowed lumen and rigid aortic wall resulting from this vasculopathy provided an increased afterload leading to cardiac failure.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 2000

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