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Anomalous origin of right pulmonary artery: diagnosis, treatment, and follow-up in an adult patient

Published online by Cambridge University Press:  06 July 2020

Susan Pumacayo-Cárdenas*
Affiliation:
Departamento de Tomografía cardiaca, Instituto nacional de cardiología Ignacio Chávez, Ciudad de México, México
Moises Jimenez-Santos
Affiliation:
Departamento de Tomografía cardiaca, Instituto nacional de cardiología Ignacio Chávez, Ciudad de México, México
Edgar Quea-Pinto
Affiliation:
Departamento de cardiología intervencionista de cardiopatías congénitas, Instituto nacional de cardiología Ignacio Chávez, Ciudad de México, México
*
Author for correspondence: Susan Pumacayo-Cárdenas, Belisario Domínguez Sección 16, Belisario Domínguez Secc 16, Tlalpan, CDMX. Tel: +51979791469. E-mail: pumacayocardenas@gmail.com

Abstract

Anomalous origin of a branch pulmonary artery from the aorta is a rare malformation, accounting for 0.12% of all congenital heart defects. We present the case of a 43-year-old man with an anomalous origin of the right pulmonary artery (AORPA) from the ascending aorta. Reimplantation of the right pulmonary artery was carried out successfully, with favourable evolution in the medium-term follow-up. It is the first described case that receives corrective treatment in adulthood with a favourable evolution.

Type
Brief Report
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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