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Unilateral absence of the pulmonary artery: a report of two cases that presented different clinical courses

Published online by Cambridge University Press:  20 November 2014

Ryota Higeno ,
Noboru Inamura  and
Futoshi Kayatani
Ryota Higeno*
Affiliation:
Department of Pediatric Cardiology, Osaka Medical Center and Research Institute for Maternal and Child Health, Osaka, Japan
Noboru Inamura
Affiliation:
Department of Pediatric Cardiology, Osaka Medical Center and Research Institute for Maternal and Child Health, Osaka, Japan
Futoshi Kayatani
Affiliation:
Department of Pediatric Cardiology, Osaka Medical Center and Research Institute for Maternal and Child Health, Osaka, Japan
*
Correspondence to: Dr R. Higeno, MD, Department of Pediatric Cardiology, Osaka Medical Center and Research Institute for Maternal and Child Health; 840 Murodo-cho, Izumi, Osaka 594-1101, Japan. Tel: +81-725-56-1220; Fax: +81-725-56-5682; E-mail: higeno@ped.med.osaka-u.ac.jp
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Abstract

We recently diagnosed two cases of isolated unilateral absence of the pulmonary artery just after birth. Through the therapy, we could not prevent obstruction of the pulmonary artery and lead to complications. There have been no symptoms attributed to isolated unilateral absence of the pulmonary artery so far. We should carefully consider the strategy for therapeutic intervention for asymptomatic cases.

Keywords

Absence of the pulmonary arteryprostaglandin E1computed tomographyemphysema
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 7 , October 2015 , pp. 1399 - 1402
Copyright
© Cambridge University Press 2014 

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