Hostname: page-component-78c5997874-s2hrs Total loading time: 0 Render date: 2024-11-01T02:15:19.385Z Has data issue: false hasContentIssue false
  • English
  • Français

Pentalogy of Cantrell with double-outlet right ventricle: a case of surgical correction

Published online by Cambridge University Press:  21 December 2010

Yoshio Ootaki ,
James Strainic  and
Ross M. Ungerleider
Yoshio Ootaki*
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
James Strainic
Affiliation:
Division of Pediatric Cardiology, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
Ross M. Ungerleider
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
*
Correspondence to: Dr Y. Ootaki, Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, 11100 Euclid Avenue, Cleveland, Ohio 44106, United States of America. Tel: 216 844 3058; Fax: 216 844 3517; E-mail: y.ootaki@nifty.com
Get access Rights & Permissions [Opens in a new window]

Abstract

Pentalogy of Cantrell is characterised by a combination of severe defects in the middle of the chest including the sternum, diaphragm, heart, and abdominal wall. Mortality rate after cardiac surgery is usually high. We report a successful total correction of the cardiac defects in a case of Pentalogy of Cantrell with a double-outlet right ventricle prior to abdominal wall defect repair.

Keywords

Congenital cardiac defectcardiac surgeryomphalocele
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 2 , April 2011 , pp. 235 - 237
Copyright
Copyright © Cambridge University Press 2010

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Cantrell, JR, Haller, JA, Ravitch, MM. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart. Surg Gynecol Obstet 1958; 107: 602–614.Google ScholarPubMed
2. Vazquez-Jimenez, JF, Muehler, EG, Daebritz, S, et al. Cantrell's syndrome: a challenge to the surgeon. Ann Thorac Surg 1998; 65: 1178–1185.CrossRefGoogle ScholarPubMed
3. St Louis, JD. Pentalogy of Cantrell associated with hypoplastic left heart syndrome and herniation of the ventricular mass into the abdominal cavity. Interact Cardiovasc Thorac Surg 2006; 5: 200–201.CrossRefGoogle ScholarPubMed
4. van Hoorn, JH, Moonen, RM, Huysentruyt, CJ, van Heurn, LW, Offermans, JP, Mulder, AL. Pentalogy of Cantrell: two patients and a review to determine prognostic factors for optimal approach. Eur J Pediatr 2008; 167: 29–35.CrossRefGoogle Scholar
5. Takaya, J, Kitamura, N, Tsuji, K, et al. Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient. Eur J Pediatr 2008; 167: 103–105.CrossRefGoogle Scholar
6. Korver, AM, Haas, F, Freund, MW, Strengers, JL. Pentalogy of Cantrell: successful early correction. Pediatr Cardiol 2008; 29: 146–149.CrossRefGoogle ScholarPubMed
7. Gao, Z, Duan, QJ, Zhang, ZW, Ying, LY, Ma, LL. Images in cardiovascular medicine: Pentalogy of Cantrell associated with thoracoabdominal ectopia cordis. Circulation 2009; 119: e483–e485.CrossRefGoogle ScholarPubMed
8. O'Gorman, CS, Tortoriello, TA, McMahon, CJ. Outcome of children with Pentalogy of Cantrell following cardiac surgery. Pediatr Cardiol 2009; 30: 426–430.CrossRefGoogle ScholarPubMed