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Infantile scimitar syndrome with severe pulmonary hypertension: successful treatment with coil embolization of the systemic arterial supply to the sequestered lung

Published online by Cambridge University Press:  19 August 2008

Jean-Pierre Pfammatter*
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
Ingrid Luhmer
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
Hans Carlo Kallfelz
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
*Corresponding
Dr Jean-Pierre Pfammatter, MD. Division of Pediatric CardiologyChildren's Hospital, Freiburgstrasse, CH-3010 Berne, Switzerland. Fax: ++41 31 632 9748

Abstract

Scimitar syndrome is a rare cardiopulmonary malformation. Presentation in infancy is usually associated with pulmonary hypertension and severe symptoms. We discuss treatment of such an infant. Two abnormal systemic vessels supplying the sequestered lower part of the right lung were embolized using catheter-inserted coils. The patent arterial duct was surgically ligated. These procedures resulted in a significant reduction of the shunt and the level of pulmonary hypertension, as well as in an impresssive improvement of symptoms.

Type
Brief-Reports
Copyright
Copyright © Cambridge University Press 1997

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References

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Infantile scimitar syndrome with severe pulmonary hypertension: successful treatment with coil embolization of the systemic arterial supply to the sequestered lung
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