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The impact, and surgical implications, of isolated anomalous connection of one pulmonary vein

Published online by Cambridge University Press:  01 October 2007

Masahiro Koh
Department of Cardiovascular Surgery, National Cardiovascular Center, Osaka, Japan
Hideki Uemura
Department of Cardiothoracic Surgery, Royal Brompton Hospital, London, United Kingdom
Koji Kagisaki*
Department of Cardiovascular Surgery, National Cardiovascular Center, Osaka, Japan
Correspondence to: Koji Kagisaki, Department of Cardiovascular Surgery, National Cardiovascular Center, 5-7-1 Fujishiro-dai, Suita, Osaka, 565-8565, Japan. Tel: +81 6 6833 5012; Fax: +81 6 6872 7486; E-mail:


Partially anomalous pulmonary venous connection of a solitary pulmonary vein in the setting of an intact atrial septum is often subclinical, and the indications for surgical repair are controversial. Here we describe a patient who developed a significant shunt over a period of 10-years. Flow through the anomalously connected pulmonary segment depends on the difference of pressure between the right and left atrium, and may increase with age.

Brief Report
Copyright © Cambridge University Press 2007

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