Skip to main content Accessibility help
×
Home
Hostname: page-component-768dbb666b-ptlz9 Total loading time: 0.276 Render date: 2023-02-02T22:40:59.233Z Has data issue: true Feature Flags: { "useRatesEcommerce": false } hasContentIssue true

Hypoplasia of the left heart with discordant ventriculoarterial connections

Published online by Cambridge University Press:  18 November 2005

Thomas Borth-Bruhns
Affiliation:
Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
Gerhard Ziemer
Affiliation:
Cardiothoracic Surgery, University Hospital, Tübingen, Germany
Michael Hofbeck
Affiliation:
Pediatric Cardiology, University Children's Hospital, Tübingen, Germany

Abstract

We report the rare combination of a severely hypoplastic left ventricle and discordant ventriculoarterial connections, with associated subpulmonary obstruction of the left ventricular outflow tract. The long tortuous arterial duct originated at an acute angle from the aorta, suggesting that the subpulmonary obstruction developed early in fetal life. Residual flow via the hypoplastic left ventricle to the pulmonary circulation after insertion of an aortopulmonary shunt resulted in haemodynamic deterioration, which was instantly reversed by closing the pulmonary trunk.

Type
Brief Report
Copyright
© 2005 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Leitner G, Hammerer I. Agenesis of the ductus arteriosus Botalli and premature closure of the foramen ovale, in combination with mitral valve atresia, hypoplastic left ventricle, transposition of the great arteries, and pulmonary valve atresia. Pathol Res Pract 1980; 170: 410419.Google Scholar
Lang D, Hofstetter R, Kupferschmid C. Hypoplastic left heart with complete transposition of the great arteries. Br Heart J 1985; 53: 650653.Google Scholar
Ho SY, Angelini A, Russell G. Pulmonary atresia with hypoplastic left ventricle. Int J Cardiol 1987; 15: 349352.Google Scholar
Oberhoffer R, Lang D, Schmaltz AA, Kupferschmid C. Hypoplastic left heart with transposition of the great arteries. Z Kardiol 1988; 77: 6468.Google Scholar
Shiono N, Takanashi Y, Yoshihara K, et al. Successful surgical treatment of total cavopulmonary connection on a 4-year-old boy with complete transposition of the great arteries and hypoplastic left ventricle. Nippon Kyobu Geka Gakkai Zasshi 1995; 43: 884888.Google Scholar
Nakata S, Imai Y, Takanashi Y, et al. A new method for the quantitative standardization of cross-sectional areas of the pulmonary arteries in congenital heart diseases with decreased pulmonary blood flow. J Thorac Cardiovasc Surg 1984; 88: 610619.Google Scholar
Abrams S, Walsh K. Arterial duct morphology with reference to angioplasty and stenting. Int J Cardiol 1993; 40: 2733.Google Scholar
Santos MA, Moll JN, Drumond C, Araujo WB, Romao N, Reis NB. Development of the ductus arteriosus in right ventricular out-flow tract obstruction. Circulation 1980; 62: 818822.Google Scholar
Mildner RJ, Kiraly L, Sreeram N. Pulmonary atresia, “intact ventricular septum”, and aortopulmonary collateral arteries. Heart 1997; 77: 173175.Google Scholar

Save article to Kindle

To save this article to your Kindle, first ensure coreplatform@cambridge.org is added to your Approved Personal Document E-mail List under your Personal Document Settings on the Manage Your Content and Devices page of your Amazon account. Then enter the ‘name’ part of your Kindle email address below. Find out more about saving to your Kindle.

Note you can select to save to either the @free.kindle.com or @kindle.com variations. ‘@free.kindle.com’ emails are free but can only be saved to your device when it is connected to wi-fi. ‘@kindle.com’ emails can be delivered even when you are not connected to wi-fi, but note that service fees apply.

Find out more about the Kindle Personal Document Service.

Hypoplasia of the left heart with discordant ventriculoarterial connections
Available formats
×

Save article to Dropbox

To save this article to your Dropbox account, please select one or more formats and confirm that you agree to abide by our usage policies. If this is the first time you used this feature, you will be asked to authorise Cambridge Core to connect with your Dropbox account. Find out more about saving content to Dropbox.

Hypoplasia of the left heart with discordant ventriculoarterial connections
Available formats
×

Save article to Google Drive

To save this article to your Google Drive account, please select one or more formats and confirm that you agree to abide by our usage policies. If this is the first time you used this feature, you will be asked to authorise Cambridge Core to connect with your Google Drive account. Find out more about saving content to Google Drive.

Hypoplasia of the left heart with discordant ventriculoarterial connections
Available formats
×
×

Reply to: Submit a response

Please enter your response.

Your details

Please enter a valid email address.

Conflicting interests

Do you have any conflicting interests? *