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Section 3 - Left-Sided Obstructive Lesions

Published online by Cambridge University Press:  09 September 2021

Laura K. Berenstain
Affiliation:
Cincinnati Children's Hospital Medical Center
James P. Spaeth
Affiliation:
Cincinnati Children's Hospital Medical Center
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Chapter
Information
Congenital Cardiac Anesthesia
A Case-based Approach
, pp. 83 - 136
Publisher: Cambridge University Press
Print publication year: 2021

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References

References

Saung, M. T., McCracken, C., Sachdeva, R., et al. Outcomes following balloon aortic valvuloplasty vs surgical valvotomy in congenital aortic valve stenosis: a meta-analysis. J Invasive Cardiol 2019; 31: E133–44.
Ewert, P., Bertram, H., Breuer, J., et al. Balloon valvuloplasty in the treatment of congenital aortic valve stenosis: a retrospective multicenter survey of more than 1000 patients. Int J Cardiol 2011; 149: 182185.
Nykanen, D. G., Forbes, T. J., Du, W., et al. CRISP: catheterization risk score for pediatrics: a report from the congenital cardiac interventional study consortium (CCISC). Catheter Cardio Inte 2016; 87: 302–9.
Ramamoorthy, C., Haberkern, C. M., Bhananker, S. M., et al. Anesthesia-related cardiac arrest in children with heart disease: data from the pediatric perioperative cardiac arrest (POCA) registry. Anesth Analg 2010; 110: 1376–82.
Odegard, K. C., Vincent, R., Baijal, R., et al. SCAI/CCAS/SPA expert consensus statement for anesthesia and sedation practice: recommendations for patients undergoing diagnostic and therapeutic procedures in the pediatric and congenital cardiac catheterization laboratory. Catheter Cardio Inte 2016; 88: 912–22.

Suggested Reading

Daaboul, D. G., Dinardo, J. A., and Nasr, V. G. Anesthesia for high-risk procedures in the catheterization laboratory. Pediatric Anesthesia 2019; 29: 491–8.
Odegard, K. C., Bergersen, L., Thiagarajan, R., et al. The frequency of cardiac arrests in patients with congenital heart disease undergoing cardiac catheterization. Anesth Analg 2014; 118: 175–82.
Vergnat, M., Asfour, B., Arenz, C., et al. Aortic stenosis of the neonate: a single-center experience. J Thorac and Cardiovasc Surg 2019; 157: 318–26.

References

Singh, G. K.. Congenital aortic valve stenosis. Children 2019; 6: 112.
Vlahos, A. P., Marx, G. R., McElhinney, D., et al. Clinical utility of Doppler echocardiography in assessing aortic stenosis severity and predicting need for intervention in children. Pediatr Cardiol 2008; 29: 507–14.
Rao, P. S.. Management of congenital heart disease: state of the art; Part I – ACYANOTIC heart defects. Children 2019; 6: 127.
Bouhout, I., Salmane, P., El-Hamamsy, I., et al. Aortic valve interventions in pediatric patients. Semin Thorac Cardiovasc Surg 2018; 31: 277–87.
Woods, R. K., Pasquali, S. K., Jacobs, M. L., et al. Aortic valve replacement in neonates and infants: an analysis of the Society of Thoracic Surgeons Congenital Heart Surgery Database. J Thorac Cardiovasc Surg 2012; 144: 1084–90.
Nelson, J. S., Pasquali, S. K., Pratt, C. N., et al. Long-term survival and reintervention after the Ross procedure across the pediatric age spectrum. Ann Thorac Surg 2015; 99: 2086–95.

Suggested Reading

Gottlieb, E. A. and Andropoulos, D. B. Anesthesia for the patient with congenital heart disease presenting for noncardiac surgery. Curr Opin Anesthesiol 2013; 26: 318–26.
Mavroudis, C., Mavroudis, C. D., and Jacobs, J. P. The Ross, Konno, and Ross-Konno operations for congenital left ventricular outflow tract abnormalities. Cardiol Young 2014; 24: 1121–33.
Stulak, J. M., Burkhart, H. M., Sundt, T. M., et al. Spectrum and outcome of reoperations after the Ross procedure. Circulation 2010; 122: 1153–58.

Suggested Reading

Bengur, A. R., Snider, A. R., Serwer, G. A., et al. Usefulness of the Doppler mean gradient in evaluation of children with aortic valve stenosis and comparison to gradient at catheterization. Am J Cardiol 1989; 64: 756–61.
Braunwald, E., Goldblatt, A., Aygen, M. M., et al. Congenital aortic stenosis. I. Clinical and hemodynamic findings in 100 patients. II Surgical treatment and the results of operation. Circulation 1963; 27: 42662.
Lopes, R., Lourenço, P., Gonçalves, A., et al. The natural history of congenital subaortic stenosis. Congenit Heart Di 2011; 6: 417–23.
Nishimura, R. A., Otto, C. M., Bobo, R. O., et al. 2014 AHA/ACC guidelines for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines. J Am Coll Cardiol 2014; 63: e57-e185.
Pickard, S. S., Geva, A., Gauvreau, K., et al. Long-term outcomes and risk factors for aortic regurgitation after discrete subvalvular aortic stenosis resection in children. Heart 2015; 101: 1547–53.
Talwar, S., Anand, A., Gupta, S. K., et al. Resection of subaortic membrane for discrete subaortic stenosis. J Card Surg 2017; 32: 43035.
Uysal, F., Bostan, O. M., Signak, I. S., et al. Evaluation of subvalvular aortic stenosis in children: a 16-year single-center experience. Pediatr Cardiol 2013; 34: 1409–14.
Vincent, W. R., Buckberg, G. D., and Hoffman, J. I. Left ventricular subendocardial ischemia in severe valvar and supravalvar aortic stenosis: a common mechanism. Circulation 1974; 49: 32633.
Vlahos, A. P., Marx, G. R., McElhinney, D., et al. Clinical utility of Doppler echocardiography in assessing aortic stenosis severity and predicting need for intervention in children. Pediatr Cardiol 2008; 29: 50714.

References

Williams, J. C. P., Barratt-Boyes, B. G., and Lowe, J. B.. Supravalvular aortic stenosis. Circulation 1961; 24: 1311–18.
Beuren, A. J., Apitz, J., and Harmjanz, D.. Supravalvular aortic stenosis in association with mental retardation and a certain facial appearance. Circulation 1962; 26: 1235–40.
Stromme, P., Bjornstad, P. G., and Ramstad, K.. Prevalence estimation of Williams syndrome. J Child Neurol 2002; 17: 269–71.
Twite, M. D., Stenquist, S., and Ing, R. J.. Williams syndrome. Pediatr Anesth 2019; 29: 483–90.
Taylor, D. and Habre, W.. Risk associated with anesthesia for noncardiac surgery in children with congenital heart disease. Pediatr Anesth 2019; 29: 426–34.
Ewart, A. K., Morris, C. A., Atkinson, D., et al. Hemizygosity at the elastin locus in a developmental disorder, Williams syndrome. Nat Genet 1993; 5: 1116.
Urbán, Z., Zhang, J., Davis, E. C., et al. Supravalvular aortic stenosis: genetic and molecular dissection of a complex mutation in the elastin gene. Hum Genet 2001; 109: 512–20.
Collins, R. T., Kaplan, P., Somes, G. W., et al. Long-term outcomes of patients with cardiovascular abnormalities and Williams syndrome. Am J Cardiol 2010; 105: 874–8.
Horowitz, P. E., Akhtar, S., Wulff, J. A., et al. Coronary artery disease and anesthesia-related death in children with Williams syndrome. J Cardiothorac Vasc Anesth 2002; 16: 739–41.
Baum, V. C. and O’Flaherty, J. E.. Anesthesia for Genetic, Metabolic, and Dysmorphic Syndromes of Childhood. 3rd ed. Philadelphia: Wolters Kluwer 2015; 475–6.
Collins, R. T., Aziz, P. F., Gleason, M. M., et al. Abnormalities of cardiac repolarization in Williams syndrome. Am J Cardiol 2010; 106: 1029–33.
Latham, G. J., Ross, F. J., Eisses, M. J., et al. Perioperative morbidity in children with elastin arteriopathy. Pediatr Anesth 2016; 26: 926–35.
Wessel, A., Gravenhorst, V., Buchhorn, R., et al. Risk of sudden death in the Williams-Beuren syndrome. Am J Med Genet 2004; 127A: 234–7.
Hornik, C. P., Collins, R. T., Jaquiss, R. D. B., et al. Adverse cardiac events in children with Williams syndrome undergoing cardiovascular surgery: an analysis of the Society of Thoracic Surgeons Congenital Heart Surgery Database. J Thorac Cardiovasc Surg 2015; 149: 1516–22.
Bird, L. M., Billman, G. F., Lacro, R. V., et al. Sudden death in Williams syndrome: report of ten cases. J Pediatr 1996; 129: 926–31.
Castañeda, A. R., Jonas, R. A., Mayer, J. E., et al. Cardiac Surgery of the Neonate and Infant. 1st ed. Philadelphia: W.B. Saunders, 1994; 327–32.
Pober, B. R.. Williams-Beuren syndrome. N Engl J Med 2010; 362: 239–52.
Medley, J., Russo, P., and Tobias, J. D.. Perioperative care of the patient with Williams syndrome. Pediatr Anesth 2005; 15: 243–7.
Committee on Genetics. American Academy of Pediatrics: healthcare supervision for children with Williams syndrome. Pediatrics 2001; 107: 1192–204.
Brown, M. L., Nasr, V. G., Toohey, R., et al. Williams syndrome and anesthesia for non-cardiac surgery: high risk can be mitigated with appropriate planning. Pediatr Cardiol 2018; 39: 1123–8.
Collins, R. T., Collins, M. G., Schmitz, M. L., et al. Peri-procedural risk stratification and management of patients with Williams syndrome. Congenit Heart Dis 2017; 12: 133–42.

Suggested Reading

Brown, M. L., Nasr, V. G., Toohey, R., et al. Williams syndrome and anesthesia for non-cardiac surgery: high risk can be mitigated with appropriate planning. Pediatr Cardiol 2018; 39: 1123–28.
Burch, T. M., McGowan, F. X., Kussman, B. D., et al. Congenital supravalvular aortic stenosis and sudden death associated with anesthesia: what’s the mystery? Anesth Analg 2008; 107: 1848–54.
Collins, R. T., Collins, M. G., Schmitz, M. L., et al. Peri-procedural risk stratification and management of patients with Williams syndrome. Congenit Heart Dis 2017; 12: 133–42.
Latham, G. J., Ross, F. J., Eisses, M. J., et al. Perioperative morbidity in children with elastin arteriopathy. Pediatr Anesth 2016; 26: 926–35.
Matisoff, A. J., Olivieri, L., Schwartz, J. M., et al. Risk assessment and anesthetic management of patients with Williams syndrome: a comprehensive review. Pediatr Anesth 2015; 25: 1207–15.
Pober, B. R. Williams-Beuren syndrome. N Engl J Med 2010; 362: 239–52.
Twite, M. D., Stenquist, S., and Ing, R. J. Williams syndrome. Pediatr Anesth 2019; 29: 483–90.

References

Poliac, L. C., Barron, M. E., and Maron, B. J.. Hypertrophic cardiomyopathy. Anesthesiology 2006; 104 : 183–92.
Cooper, R. M., Raphael, C. E., Liebregts, M., et al. New developments in hypertrophic cardiomyopathy. Can J Cardiol 2017; 33: 1254–65.
Maron, B. J., Maron, M. S., and Semsarian, C.. Genetics of hypertrophic cardiomyopathy after 20 years: clinical perspectives. J Am Coll Cardiol 2012; 60: 705–15.
Varnava, A. M., Elliott, P. M., Mahon, N., et al. Relation between myocyte disarray and outcome in hypertrophic cardiomyopathy. Am J Cardiol 2001; 88: 275–79.
Johansson, B., Morner, S., Waldenstrom, A., et al. Myocardial capillary supply is limited in hypertrophic cardiomyopathy: a morphological analysis. Int J Cardiol 2008; 126: 252–7.
Colan, S. D., Lipshultz, S. E., Lowe, A. M., et al. Epidemiology and cause-specific outcome of cardiomyopathy in children. Findings from the Pediatric Cardiomyopathy Registry. Circulation 2007; 115: 773–81.
Maron, M. S., Maron, B. J., Harrigan, C., et al. Hypertrophic cardiomyopathy phenotype revisited after 50 years with cardiovascular magnetic resonance. J Am Coll Cardiol 2009; 54: 220–8.
Maron, B. J. and Maron, M. S.. Hypertrophic cardiomyopathy. Lancet 2013; 381: 242–55.
Gersh, B. J., Maron, B. J., Dearani, J. A., et al. 2011 ACCF/AHA guideline for the diagnosis and treatment of hypertrophic cardiomyopathy: Executive Summary, a Report of the American College of Cardiology Foundation/American Heart Association Task Force on Practice Guidelines. J Am Coll Cardio 2011; 58: 2703–38.
Hreybe, H., Zahid, M., Sonel, A., et al. Noncardiac surgery and the risk of death and other cardiovascular events in patients with hypertrophic cardiomyopathy. Clin Cardiol 2006; 29: 65–8.
Norrish, B., Forshaw, N., Woo, C., et al. Outcomes following general anesthesia in children with hypertrophic cardiomyopathy. Arch Dis Child 2019; 104: 471–5.
Dhillon, A., Khanna, A., Randhawa, M. S., et al. Perioperative outcomes of patients with hypertrophic cardiomyopathy undergoing non-cardiac surgery. Heart 2016; 102: 1627–32.
Crossley, G. H., Poole, J. E., Rozner, M. A., et al. The Heart Rhythm Society (HRS)/American Society of Anesthesiologists (ASA) Expert Consensus Statement on the perioperative management of patients with implantable defibrillators, pacemakers and arrhythmia monitors. Heart Rhythm 2011; 8: 1114–54.
Madigan, J. D., Choudhri, A. F., Chen, J., et al. C. Surgical management of the patient with an implanted cardiac device Ann Surg 1999; 230: 639–47.

Suggested Reading

Dhillon, A., Khanna, A., Randhawa, M. S., et al. Perioperative outcomes of patients with hypertrophic cardiomyopathy undergoing non-cardiac surgery. Heart 2016; 102: 1627–32.
Norrish, B., Forshaw, N., Woo, C., et al. Outcomes following general anesthesia in children with hypertrophic cardiomyopathy. Arch Dis Child 2019; 104: 471–75.

References

Fox, E. B., Latham, G. J., Ross, F. J., et al. Perioperative and anesthetic management of coarctation of the aorta. Semin Cardiothorac Vasc Anesth 2019; 23: 221–4.
Boris, J. R.. Primary-care management of patients with coarctation of the aorta. Cardiol Young 2016; 26: 1537–42.
Padua, L. M. S., Garcia, L. C., Rubira, C. J., et al. Stent placement versus surgery for coarctation of the thoracic aorta (review). Cochrane Database Syst Rev 2012; 5: 118.
Astengo, M., Berntsson, C., Johnsson, A. A., et al. Ability of noninvasive criteria to predict hemodynamically significant aortic obstruction in adults with coarctation of the aorta. Congenit Heart Dis 2017; 12: 174–80.
Stout, K. K., Daniels, C. J., Aboulhosn, J. A., et al. 2018 AHA/ACC Guideline for the management of adults with congenital heart disease. J Am Coll Cardiol 2019; 73: e81192.
Fiore, A. C., Fischer, L. K., Schwartz, T., et al. Comparison of angioplasty and surgery for neonatal aortic coarctation. Ann Thorac Surg 2005; 80: 1659–65.
Koh, J. L. and Gries, H.. Perioperative management of pediatric patients with craniosynostosis. Anesthesiol Clin 2007; 25: 465–81.
Pearson, A. and Matava, C. T.. Anaesthetic management for craniosynostosis repair in children. BJA Educ 2016; 16: 410–16.

Suggested Reading

Fox, E. B., Latham, G. J., Ross, F. J., et al. Perioperative and anesthetic management of coarctation of the aorta. Semin Cardiothorac Vasc Anesth 2019; 23: 221–4.
Koh, J. L. and Gries, H. Perioperative management of pediatric patients with craniosynostosis. Anesthesiol Clin 2007; 25: 465–81.
Pearson, A. and Matava, C. T. Anaesthetic management for craniosynostosis repair in children. BJA Educ 2016; 16: 410–16.

References

Shone, J. D., Sellers, R. D., Anderson, R. C., et al. The developmental complex of “parachute mitral valve,” supravalvular ring of left atrium, subaortic stenosis, and coarctation of aorta. Am J Cardiol 1963; 11: 714–25.
Ikemba, C. M., Eidem, B. W., Fraley, J. K., et al. Mitral valve morphology and morbidity/mortality in Shone’s complex. Am J Cardiol 2005; 95: 541–3.
Grimaldi, A., Vermi, A. C., Ho, S. Y., et al. Surgical outcome of partial Shone complex. Interact Cardiovasc Thorac Surg 2012; 14: 440–4.
Marino, B. S., Kruge, L. E., Cho, C. J., et al. Parachute mitral valve: morphologic descriptors, associated lesions, and outcomes after biventricular repair. J Thorac Cardiovasc Surg 2009; 137: 385–93.
Oosthoek, P. W., Wenink, A. C., Wisse, L. J., et al. Development of the papillary muscles of the mitral valve: morphogenetic background of parachute-like asymmetric mitral valves and other mitral valve anomalies. J Thorac Cardiovasc Surg 1998; 116: 3646.
Brauner, R. A., Laks, H., Drinkwater, D. C., et al. Multiple left heart obstructions (Shone’s anomaly) with mitral valve involvement: long-term surgical outcome. Ann Thorac Surg 1997; 64: 721–9.
Jenkins, N. P. and Ward, C.. Coarctation of the aorta: natural history and outcome after surgical treatment. QJM 1999; 92: 365–71.
Nicholson, G. T., Kelleman, M. S., De la Uz, C. M., et al. Late outcomes in children with Shone’s complex: a single-centre, 20-year experience. Cardiol Young 2017; 27: 697705.
Ramamoorthy, C., Haberkern, C. M., and Bhananker, S. M.. Anesthesia-related cardiac arrest in children with heart disease: data from the Pediatric Perioperative Cardiac Arrest (POCA) registry. Anesth Analg 2010; 110: 1376–82.
Relland, L. M., Tobias, J. D., Martin, D., et al. Ultrasound-guided rectus sheath block, caudal analgesia, or surgical site infiltration for pediatric umbilical herniorrhaphy: a prospective, double-blinded, randomized comparison of three regional anesthetic techniques. J Pain Res 2017; 10: 2629–34.

Suggested Reading

Atkinson, T. M., Giraud, G. D., Togioka, B. M., et al. Cardiovascular and ventilatory consequences of laparoscopic surgery. Circulation 2017; 135: 700–10.
Friesen, R. H. Anesthetic drugs in congenital heart disease. Semin Cardiothorac Vasc Anesth 2014; 18: 363–70.
Schimke, A., Majithia, A., Baumgartner, R., et al. Intervention and management of congenital left heart obstructive lesions. Curr Treat Options Cardiovasc Med 2013; 15: 632–45.
Shone, J. D., Sellers, R. D., Anderson, R. C., et al. The developmental complex of “parachute mitral valve,” supravalvular ring of left atrium, subaortic stenosis, and coarctation of aorta. Am J Cardiol 1963; 11: 714–25.
Spaeth, J. P. and Loepke, A. W. Anesthesia for left-sided obstructive lesions. In Andropoulos, D. B., Stayer, S., Mossad, E. B., et al., eds. Anesthesia for Congenital Heart Disease, 3rd ed. Hoboken, NJ: John Wiley & Sons, 2015; 497515.

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