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Gargoylism (Hurler's Disease): A Neuropathological Report

Published online by Cambridge University Press:  08 February 2018

D. Naidoo*
Affiliation:
From the Department of Neuropathology, Institute of Psychiatry, Maudsley Hospital, University of London

Extract

Hurler's disease is characterized by chondro-dystrophic skeletal changes, corneal opacities, hepatosplenomegaly and mental defect. The skeletal changes are such that the patient presents a large head, grotesque facies, deformed limbs and kyphosis.

Type
Part I.—Original Articles
Copyright
Copyright © Royal College of Psychiatrists, 1953 

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