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Vestibular nerve dysfunction and decompression in Engelmann's disease

  • William P. L. Hellier (a1) and Gerald B. Brookes (a1)

Abstract

Vestibular nerve dysfunction as the major neuro-otological symptom in one of the osteopetrosis group of bone disorders is unusual. We describe a patient with Engelmann's disease who presented in this manner and who benefited from an eighth nerve decompression procedure. Surgical decompression of the internal auditory meatus to relieve vertigo has to our knowledge not been previously reported in this condition.

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Corresponding author

Address for correspondence: Mr. G. B. Brookes F.R.C.S., Consultant ENT and Neuro-otological Surgeon, National Hospital for Neurology and Neurosurgery, Queen Square, London WC1N 3BG.

References

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Engelmann, G. (1929) Ein Fall von Osteopathia hyperostotica (sclerotisans) multiplex infantalis. Fortschritte auf dem Gebiete der Röntgenstrahlen und der Nuklearmedizin 11011106.
Hamersma, H. (1977) Facial nerve paralysis in the osteopetroses In Facial Nerve Surgery. Aesulapius Publishing Co. Birmingham, Ala. pp 555572.
Hamersma, H., May, M. (1986) Osteopetrosis and facial palsy In The Facial Nerve. (May, M. ed.), Thieme Inc., New York, pp 469476.
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Sparkes, R. S., Graham, C. B. (1972) Camurati-Engelmann disease. Genetics and clinical manifestations with a review of the literature. Journal of Medical Genetics 9: 7385.

Keywords

Vestibular nerve dysfunction and decompression in Engelmann's disease

  • William P. L. Hellier (a1) and Gerald B. Brookes (a1)

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