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Vestibular nerve dysfunction and decompression in Engelmann's disease

  • William P. L. Hellier (a1) and Gerald B. Brookes (a1)


Vestibular nerve dysfunction as the major neuro-otological symptom in one of the osteopetrosis group of bone disorders is unusual. We describe a patient with Engelmann's disease who presented in this manner and who benefited from an eighth nerve decompression procedure. Surgical decompression of the internal auditory meatus to relieve vertigo has to our knowledge not been previously reported in this condition.


Corresponding author

Address for correspondence: Mr. G. B. Brookes F.R.C.S., Consultant ENT and Neuro-otological Surgeon, National Hospital for Neurology and Neurosurgery, Queen Square, London WC1N 3BG.


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Vestibular nerve dysfunction and decompression in Engelmann's disease

  • William P. L. Hellier (a1) and Gerald B. Brookes (a1)


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