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Plexiform schwannoma of the cheek

  • Giacinto M. Mannarà (a1), Filippo C. La Rosa (a1) and Filippo Marino (a2)


We present a case of subcutaneous plexiform schwannoma, a rare benign peripheral nerve sheath tumour characterized by a multinodular and plexiform growth pattern. A review of the literature was performed to identify the relationship between plexiform schwannoma and neurofibromatosis types 1 and 2, and schwannomatosis.

It is also important to distinguish plexiform schwannoma from plexiform neurofibroma, a particular type 1 neurofibromatosis lesion, because of the propensity of the latter for malignant degeneration.


Corresponding author

Address for correspondence: Giacinto M. Mannarà, M.D., Department of Otolaryngology – Head and Neck Surgery, Nuovo Policlinico, Via Giustiniani 2, 35100 Padua, Italy. Fax: 0039 49 8752266


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Plexiform schwannoma of the cheek

  • Giacinto M. Mannarà (a1), Filippo C. La Rosa (a1) and Filippo Marino (a2)


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