Skip to main content Accessibility help
×
Home

Inherited degenerative chondropathy – an autosomal dominant new clinical entity: report two cases and follow-up of four cases

  • Mary Kurien (a1), M. S. Seshadri (a2) and Anand Zachariah (a2)

Abstract

Four cases of the rare disorder, inherited degenerative chondropathy have been previously reported (Kurien et al., 1989). A five-year follow-up of these patients and two additional cases are presented in this report. The progress of this disease appears to be arrested after regulardapsone therapy and there was no other organ involvement noted during the follow-up period.

Copyright

Corresponding author

Address for correspondence: Dr Mary Kurien, M.B.B.S., D.L.O., M.S., Associate Professor, Department of ENT, Christian Medical College Hospital,Vellore, Tamil Nadu 632004, South India.

References

Hide All
Bauby, F, Suc, B., Vix, J.. Rostykus, P.. Dumas, B.. Douet, F., (1991) Les manifestations ORL de Iapolychrondritc chronique atrophiaute. A propos d'une observation. Annals D Otolarvngologie et de Chiritrgie Cervico-Faciale. 108(1): 6062.
Cyril, M. G., Joseph, P. L. III, (1993) Tracheobronchial and eosphageal manifestations of systemic diseases. In Oiolaryngology-Head and Neck Surgery. 2nd Edition. (Charles, W. C., John, M. F., Lee, A. H., Charles, J. K., David, F. S., eds.). ch. 125. Mosby Year Book. Inc.. St Louis. pp 23002301.
Gouet, D.. Marechud, R.. Neau, J. P.. Abadie, J. C.. Rossi, F.Sudre, Y. (1984) Polychondrite chronique atrophiante. Analyse critique de l'efficacite therapeutique de Ia dapsone: Deux observations. Presse Medicale 13: 723726.
Kurien, M., Seshadri, M. S., Raman, R.. Sen Bhanu, T. (1989) Inherited nasal and laryngeal degenerative chrondropathy. Archives of Otolaryngologv, Head and Neck Sitrgery 115: 746748.
McAdam, L. P., O'Hanlan, M. A., Bluestone, R.. Pearson, C. M. (1976) Relapsing polychondritis: prospective study of 23 patients and review of literature. Medicine 55: 193215.
McKusick, V. A. (1966) Heritable Disorders of Connective Tissue, 3rd Edition, Ch. 10, C. V. Mosby Co., St Louis, pp 400480.
Moloney, J. R. (1978) Relapsing polychondritis: its otolaryngological manifestations Journalof Laryngology and Otology 92: 915.

Keywords

Inherited degenerative chondropathy – an autosomal dominant new clinical entity: report two cases and follow-up of four cases

  • Mary Kurien (a1), M. S. Seshadri (a2) and Anand Zachariah (a2)

Metrics

Full text views

Total number of HTML views: 0
Total number of PDF views: 0 *
Loading metrics...

Abstract views

Total abstract views: 0 *
Loading metrics...

* Views captured on Cambridge Core between <date>. This data will be updated every 24 hours.

Usage data cannot currently be displayed