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Auditory rehabilitation in neurofibromatosis type 2: a case for cochlear implantation

  • Robert H. Temple (a1), Patrick R. Axon (a1), Richard T. Ramsden (a1), Nesil Keles (a2), Kemal Deger (a2) and Emre Yücel (a2)...


Cochlear implantation has a limited but definite role in the rehabilitation of certain neurofibromatosis type 2 (NF2) patients. The presence of a dead ear either before, or after, tumour removal does not necessarily imply loss of function in the eighth nerve; in some instances the hearing loss will be cochlear. Promontory or round window electrical stimulation may help to identify those individuals with surviving eighth nerve function. In such patients multichannel cochlear implantation promises a better level of audition than the auditory brain stem implant. This paper highlights such a case and the management problems are discussed.


Corresponding author

Address for correspondence: Mr R. H. Temple, Department of Otolaryngology, Manchester Royal Infirmary, Oxford Road, Manchester M13 9WL. Fax: 0161 276 8511


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Auditory rehabilitation in neurofibromatosis type 2: a case for cochlear implantation

  • Robert H. Temple (a1), Patrick R. Axon (a1), Richard T. Ramsden (a1), Nesil Keles (a2), Kemal Deger (a2) and Emre Yücel (a2)...


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