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Asymptomatic superior semicircular canal dehiscence

Published online by Cambridge University Press:  27 October 2021

L Verrecchia*
Affiliation:
ENT Unit, Department of Clinical Science, Intervention and Technology – CLINTEC, Karolinska Institutet, Solna ENT Department, Audiology and Neurotology Section, Karolinska University Hospital, Huddinge, Sweden
K Edholm
Affiliation:
Department of Neuroradiology, Karolinska University Hospital, Huddinge, Sweden
M Pekkari
Affiliation:
ENT Unit, Department of Clinical Science, Intervention and Technology – CLINTEC, Karolinska Institutet, Solna ENT Department, Audiology and Neurotology Section, Karolinska University Hospital, Huddinge, Sweden
*
Author for correspondence: Dr Luca Verrecchia, ENT Unit, Department of Clinical Science, Intervention and Technology – CLINTEC, Karolinska Institutet, Karolinska University Hospital, B61, 14186Huddinge, Sweden E-mail: luca.verrecchia@ki.se Fax: +46 85 858 7353

Abstract

Objective

To describe a case of asymptomatic superior semicircular canal dehiscence.

Method

Clinical case report.

Results

A 50-year-old man presenting with right-sided Ménière´s disease also showed an enhanced response on vestibular evoked myogenic potential testing for the left ear. Unilateral left-sided superior semicircular canal bone dehiscence was clearly visualised on a subsequent temporal bone computed tomography scan. These findings were consistent with superior canal dehiscence syndrome. However, the patient did not complain of any specific superior canal dehiscence syndrome symptoms. Given that vestibular evoked myogenic potential testing may detect asymptomatic forms of superior canal dehiscence, as noted in this case, such testing seems to exhibit reduced specificity for superior canal dehiscence syndrome.

Conclusion

An enhanced response on vestibular evoked myogenic potential testing in isolation appears to be a weaker indicator of superior canal dehiscence syndrome, and rather a marker of superior semicircular canal dehiscence.

Type
Clinical Records
Copyright
Copyright © The Author(s), 2021. Published by Cambridge University Press

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Footnotes

Dr L Verrecchia takes responsibility for the integrity of the content of the paper

References

Ward, BK, Carey, JP, Minor, LB. Superior canal dehiscence syndrome: lessons from the first 20 years. Front Neurol 2017;8:177CrossRefGoogle ScholarPubMed
Brantberg, K, Verrecchia, L. Effectiveness of different click stimuli in diagnosing superior canal dehiscence using cervical vestibular evoked myogenic potentials. Acta Otolaryngol 2012;132:1077–83CrossRefGoogle ScholarPubMed
Lopez-Escamez, JA, Carey, J, Chung, WH, Goebel, JA, Magnusson, M, Mandalà, M et al. Diagnostic criteria for Menière's disease. J Vestib Res 2015;25:17CrossRefGoogle ScholarPubMed
Noij, KS, Wong, K, Duarte, MJ, Masud, S, Dewyer, NA, Herrmann, BS et al. Audiometric and cVEMP thresholds show little correlation with symptoms in superior semicircular canal dehiscence syndrome. Otol Neurotol 2018;39:1153–62CrossRefGoogle ScholarPubMed
Mittmann, P, Ernst, A, Seidl, R, Skulj, AF, Mutze, S, Windgassen, M et al. Superior canal dehiscence: a comparative postmortem multislice computed tomography study. OTO Open 2018;2:2473974X18793576CrossRefGoogle ScholarPubMed