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Abilities and attainment in Smith-Magenis syndrome

Published online by Cambridge University Press:  18 December 2001

Orlee Udwin
Affiliation:
Child Clinical Psychology, Child and Adolescent Mental Health Services, UK.
Carolyn Webber
Affiliation:
Child Clinical Psychology, Child and Adolescent Mental Health Services, UK.
Isobel Horn
Affiliation:
Adult Mental Health, South London and Maudsley NHS Trust, London, UK.
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Abstract

This study reports on cognitive abilities and attainment in 29 children and 21 adults with Smith-Magenis syndrome. There were 13 boys and 16 girls aged 6 to 16 years, and nine men and 12 women aged 16 to 52 years. All had mild to severe learning disabilities with no differences overall between verbal and performance skills, but with a particular profile of cognitive strengths and weaknesses. Levels of attainment and of adaptive behaviour were strikingly low, and the group of adults emerged as much more dependent on carers than might have been expected from their general level of intellectual functioning. Reasons for this discrepancy are explored in terms of the severe behavioural difficulties characteristic of the syndrome.

Type
Original Articles
Copyright
© 2001 Mac Keith Press

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