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Unsuccessful two-stage correction despite appropriate surgery in a case with disconnection (so-called absence) of the right pulmonaty artery

Published online by Cambridge University Press:  19 August 2008

Hans P. Gildein ,
Götz von Bernuth  and
Rolf Mocellin
Hans P. Gildein*
Affiliation:
From the Department of Pediatric Cardiology, University of Freiburg, Freiburg
Götz von Bernuth
Affiliation:
Department of Pediatric Cardiology, The Hospital for Pediatric Cardiology, Rheinisch-Wesifdlische Technische Hochschule Aachen, Aachen
Rolf Mocellin
Affiliation:
From the Department of Pediatric Cardiology, University of Freiburg, Freiburg
*
Dr. Hans P. Gildein, Abteilung Pädiatrische Kardiologie, UniversitSts-Kinderklinik, Mahildenstr. 1, 79106 Freiburg, Germany. Tel. 0761/270-4318; Fax. 0761/270-4481.
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Summary

A right-sided modified Blalock-Taussig anastomosis was created using a 5 mm Gore-Tex tube in a 4½ month old infant with unilateral “absence” of the right pulmonary artery. Wide patency of the shunt was confirmed shortly after by angiography, but rarefaction of the peripheral right pulmonary arteries was seen at the age of 2½ years, when corrective surgery was performed. Postoperative hypoperfusion of the right lung, along with severe pulmonary vascular abnormalities seen in a lung biopsy, indicated failure of the two-stage correction in spite of appropriate surgery.

Keywords

Absent pulmonary arterysurgerypulmonary vascular disease
Type
Brief Reports
Information
Cardiology in the Young , Volume 3 , Issue 4 , October 1993 , pp. 445 - 447
Copyright
Copyright © Cambridge University Press 1993

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