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Truncus arteriosus communis in combination with cor triatriatum sinsitrum

  • Elmar Klusmeier (a1), Nikolaus A. Haas (a1) and Eugen Sandica (a2)


Truncus arteriosus communis is a rare CHD, accounting for only 1% of all congenital cardiac abnormalities. It has been associated with other malformations of the heart, mainly truncal valve (bicuspid/quadricuspid) and aortic arch abnormalities such as right, interrupted, and hypoplastic aortic arch. Cor tratriatrum sinistrum is another rare CHD, and it has been associated with other cardiac defects such as anomalous pulmonary venous drainage, ventricular septal defect, coarctation of the aorta, and tetralogy of Fallot. The combination of truncus arteriosus communis and cor tratriatrum sinistrum has not been reported so far. This case study describes the diagnosis of a unique case, including these two very rare cardiac defects and the successful surgical treatment thereafter.


Corresponding author

Correspondence to: E. Klusmeier, MD, Centre for Congenital Heart Defects, Heart and Diabetes Centre North-Rhine Westfalia, Georgstrasse 11, D-32545 Bad Oeynhausen, Germany. Tel: +49 0 573 197 3641; Fax: +49 0 573 197 2131; E-mail:


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1. Reller, MD, Strickland, MJ, Riehle-Colarusso, T, et al. Prevalence of congenital heart defects in metropolitan Atlanta, 1998–2005. J Pediatr 2008; 153: 807.
2. Yu, IT, Hutchins, GM. Truncus arteriosus malformation: a developmental arrest at Carnegie stage 14. Teratology 1996; 53: 3137.
3. Van Praagh, R, Van Praagh, S. The anatomy of common aorticopulmonary trunk (truncus arteriosus communis) and its embryologic implications. A study of 57 necropsy cases. Am J Cardiol 1965; 16: 406425.
4. Samanek, M, Voriskova, M. Congenital heart disease among 815,569 children born between 1980 and 1989 and their 15 year survival: a prospective Bohemia survival study. Pediatr Cardiol 1999; 20: 411417.
5. Goel, AK, Saxena, A, Kothari, SS. Atrioventricular septal defect with cor triatriatum: case report and review of the literature. Pediatr Cardiol 1998; 19: 243245.
6. Hall, SM, Hislop, AA, Haworth, SG. Origin, differentiation, and maturation of human pulmonary veins. Am J Respir Cell Mol Biol 2002; 26: 333340.
7. Gupta, SK, Saxena, A, Ramakrishnan, S, Juneja, R, Devagourou, V. Complete transposition of great arteries with cor triatriatum: an unusual coexistence. Pediatr Cardiol 2012; 33: 11901195.
8. Litovsky, SH, Ostfeld, I, Bjornstad, PG, Van Praagh, R, Geva, T. Truncus arteriosus with anomalous pulmonary venous connection. Am J Cardiol 1999; 83: 801804.
9. Berdjis, F, Wells, WJ, Starnes, VA. Truncus arteriosus with total anomalous pulmonary venous return and interrupted arch. Ann Thorac Surg 1996; 61: 220222.
10. Van Praagh, R, Corsini, I. Cor triatriatum: pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and a study of normal development of the pulmonary vein and atrial septum in 83 human embryos. Am Heart J 1969; 78: 379405.
11. Ma, RY, Yang, ZY, Zhong, QJ, Xiao, Y. Cor triatriatum with tetralogy of Fallot and anomalous drainage of left superior vena cava: a case report and literature review Thorac Cardiovasc Surg 2012; 60: 226228; Epub 2011 21 June.
12. Campbell, KA, Hutchins, GM. Outflow tract abnormalities in atrioventricular canal malformations. Pediatr Pathol Lab Med 1995; 15: 1121.



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