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Truncus arteriosus communis in combination with cor triatriatum sinsitrum

Published online by Cambridge University Press:  30 April 2015

Elmar Klusmeier*
Affiliation:
Department for Pediatric Cardiology/Congenital Heart Defects, Centre for Congenital Heart Defects, Heart and Diabetes Centre North-Rhine Westfalia, Germany
Nikolaus A. Haas
Affiliation:
Department for Pediatric Cardiology/Congenital Heart Defects, Centre for Congenital Heart Defects, Heart and Diabetes Centre North-Rhine Westfalia, Germany
Eugen Sandica
Affiliation:
Department of Surgery for Congenital Heart Defects, Heart and Diabetes Centre North-Rhine Westfalia, Germany
*
Correspondence to: E. Klusmeier, MD, Centre for Congenital Heart Defects, Heart and Diabetes Centre North-Rhine Westfalia, Georgstrasse 11, D-32545 Bad Oeynhausen, Germany. Tel: +49 0 573 197 3641; Fax: +49 0 573 197 2131; E-mail: eklusmeier@hdz-nrw.de

Abstract

Truncus arteriosus communis is a rare CHD, accounting for only 1% of all congenital cardiac abnormalities. It has been associated with other malformations of the heart, mainly truncal valve (bicuspid/quadricuspid) and aortic arch abnormalities such as right, interrupted, and hypoplastic aortic arch. Cor tratriatrum sinistrum is another rare CHD, and it has been associated with other cardiac defects such as anomalous pulmonary venous drainage, ventricular septal defect, coarctation of the aorta, and tetralogy of Fallot. The combination of truncus arteriosus communis and cor tratriatrum sinistrum has not been reported so far. This case study describes the diagnosis of a unique case, including these two very rare cardiac defects and the successful surgical treatment thereafter.

Type
Brief Reports
Copyright
© Cambridge University Press 2015 

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